The von Willebrand factor-cleaving protease (ADAMTS-13) and the diagnosis of thrombotic thrombocytopenic purpura (TTP)

Pathophysiology of Haemostasis and Thrombosis

Volumn 33, Issue 5-6, 2003, Pages 417-421

  Kremer Hovinga, Johanna A ^a,b   Studt, Jan Dirk ^a   Lämmle, Bernhard ^a  

^a UNIVERSITY OF BERN   (Switzerland)

^b UNIVERSITY OF BERN   (Switzerland)

Author keywords

ADAMTS 13; Thrombotic thrombocytopenic purpura; Von Willebrand factor; Von Willebrand factor cleaving protease

Indexed keywords

AUTOANTIBODY; FRESH FROZEN PLASMA; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

CLINICAL FEATURE; CONFERENCE PAPER; DISEASE CLASSIFICATION; DISEASE COURSE; DISEASE SEVERITY; ENDOTHELIUM CELL; ENZYME ACTIVITY; ENZYME DEFICIENCY; ENZYME INHIBITION; FEVER; GENE MUTATION; GENETIC DISORDER; HETEROZYGOSITY; HOMOZYGOSITY; HUMAN; ISCHEMIA; KIDNEY DYSFUNCTION; MICROVASCULATURE; MORBIDITY; MORTALITY; NEUROLOGIC DISEASE; PATHOPHYSIOLOGY; PLASMAPHERESIS; PREVALENCE; PRIORITY JOURNAL; SURVIVAL RATE; THROMBOCYTE AGGREGATION; THROMBOCYTOPENIA; THROMBOGENESIS; THROMBOTIC THROMBOCYTOPENIC PURPURA; UPSHAW SCHULMAN SYNDROME;

ADAM PROTEINS; AUTOANTIBODIES; HUMANS; METALLOENDOPEPTIDASES; PURPURA, THROMBOTIC THROMBOCYTOPENIC;

EID: 14044264789     PISSN: 14248832     EISSN: None     Source Type: Journal    
DOI: 10.1159/000083839     Document Type: Conference Paper

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