Increased mitochondrial respiratory chain enzyme activities correlate with minor extent of liver damage in mice suffering from erythropoietic protoporphyria

Experimental Dermatology

Volumn 14, Issue 1, 2005, Pages 26-33

  Navarro, Susana ^a   del Hoyo, Pilar ^a   Campos, Yolanda ^a   Abitbol, Marie ^b   Morán Jiménez, María José ^a   García Bravo, María ^a   Ochoa, Pilar ^c   Grau, Montserrat ^a   Montagutelli, Xavier ^b   Frank, Jorge ^d   Garesse, Rafael ^c   Arenas, Joaquín ^a   de Salamanca, Enríquez ^a   Fontanellas, Antonio ^a  

^a HOSPITAL UNIVERSITARIO 12 DE OCTUBRE   (Spain)

^b INSTITUT PASTEUR   (France)

^c INSTITUTO DE INVESTIGACIONES BIOMÉDICAS ALBERTO SOLS   (Spain)

^d UNIVERSITY HOSPITAL RWTH AACHEN   (Germany)

Author keywords

Adenosine 5 triphosphate; Cytochrome c oxidase; Hepatic porphyria; Mitochondrial respiratory chain; Murine model; Protoporphyria

Indexed keywords

ADENOSINE TRIPHOSPHATE; AMINOLEVULINIC ACID; MITOCHONDRIAL ENZYME;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL CULTURE; CELL PROLIFERATION; CONTROLLED STUDY; CORRELATION ANALYSIS; DISEASE ASSOCIATION; DISORDERS OF MITOCHONDRIAL FUNCTIONS; ENZYME ACTIVITY; ERYTHROPOIETIC PROTOPORPHYRIA; GENE MUTATION; HISTOPATHOLOGY; HUMAN; HUMAN CELL; IN VITRO STUDY; LIVER INJURY; MITOCHONDRIAL RESPIRATION; MOUSE; NONHUMAN; STATISTICAL ANALYSIS; STATISTICAL SIGNIFICANCE; WESTERN BLOTTING;

EID: 13844310841     PISSN: 09066705     EISSN: None     Source Type: Journal    
DOI: 10.1111/j.0906-6705.2005.00248.x     Document Type: Article

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