Exfoliated human proximal tubular cells: A model of cystinosis and Fanconi syndrome

Pediatric Nephrology

Volumn 20, Issue 2, 2005, Pages 136-140

  Laube, Guido F ^a   Haq, Mushfequr R ^a   van't Hoff, William G ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

Cell culture; Cystinosin; Cystinosis; Proximal tubular cell; Renal Fanconi syndrome

Indexed keywords

CYSTINE; CYSTINOSIN; GAMMA GLUTAMYLTRANSFERASE; LECTIN; MEMBRANE PROTEIN; PROTEIN ANTIBODY; PROTEIN ZO1; UNCLASSIFIED DRUG;

ARTICLE; CELL CULTURE; CHILD; CLINICAL ARTICLE; CONCENTRATION (PARAMETERS); CONTROLLED STUDY; CYSTINOSIS; CYTOCHEMISTRY; ENZYME ASSAY; FANCONI RENOTUBULAR SYNDROME; GENE MUTATION; HUMAN; HUMAN CELL; IMMUNOCYTOCHEMISTRY; IN VITRO STUDY; KIDNEY PROXIMAL TUBULE; LOWE SYNDROME; LYSOSOME; MOLECULAR DYNAMICS; PHENOTYPE; PRIORITY JOURNAL; PROTEIN LOCALIZATION; TUBULAR DYSFUNCTION; URINALYSIS;

CELLS, CULTURED; CHILD; CHILD, PRESCHOOL; CYSTINOSIS; FANCONI SYNDROME; HUMANS; KIDNEY TUBULES, PROXIMAL; MODELS, BIOLOGICAL; OCULOCEREBRORENAL SYNDROME;

EID: 12944291013     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-004-1703-x     Document Type: Article

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