Altered terminal glycosylation and the pathophysiology of CF lung disease

Journal of Cystic Fibrosis

Volumn 3, Issue SUPPL. 2, 2004, Pages 95-96

  Rhim, Andrew D ^a   Stoykova, Lidia I ^a   Trindade, Arvind J ^a   Glick, Mary Catherine ^a   Scanlin, Thomas F ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

CFTR; Cystic fibrosis; Fucosylation; Golgi; Terminal glycosylation

Indexed keywords

FUCOSE; GLYCOCONJUGATE; GLYCOSYLTRANSFERASE; LECTIN; MUCIN; MUTANT PROTEIN; SIALIC ACID;

ARTICLE; CARBOHYDRATE ANALYSIS; CRYSTALLOGRAPHY; CYSTIC FIBROSIS; EPITHELIUM CELL; FUCOSYLATION; HUMAN; LUNG FIBROSIS; LUNG INFECTION; PATHOPHYSIOLOGY; PHENOTYPE; PROTEIN EXPRESSION; PROTEIN GLYCOSYLATION; PROTEIN PROCESSING; PSEUDOMONAS AERUGINOSA; REGULATORY MECHANISM; RESPIRATORY EPITHELIUM; SIALYLATION;

CYSTIC FIBROSIS; CYSTIC FIBROSIS TRANSMEMBRANE CONDUCTANCE REGULATOR; EPITHELIAL CELLS; GLYCOSYLATION; HUMANS; MUTATION; RESPIRATORY MUCOSA;

EID: 11044236810     PISSN: 15691993     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.jcf.2004.05.021     Document Type: Article

References (9)

1. Scanlin T.F. Glick M.C. Terminal glycosylation in cystic fibrosis Biochim. Biophys. Acta 1455 1999 241-253
2. Varki A. Cummings R. Esko J. Freeze H. Hart G. Marth J. Essentials of glycobiology 1999 Cold Spring Harbor Laboratory Press Cold Spring Harbor (NY)
3. Rhim A.D. Kothari V.A. Park P.J. Mulberg A.E. Glick M.C. Scanlin T.F. Terminal glycosylation of cystic fibrosis airway epithelial cells Glycoconj. J. 17 2000 385-391
4. Glick M.C. Kothari V.A. Liu A. Stoykova L.I. Scanlin T.F. Activity of fucosyltransferases and altered glycosylation in cystic fibrosis airway epithelial cells Biochimie 83 2001 743-747
5. Scanlin T.F. Glick M.C. Terminal glycosylation and disease: Influence on cancer and cystic fibrosis Glycoconj. J. 17 2000 617-626
6. Stoykova L.I. Liu A. Scanlin T.F. Glick M.C. Alpha1,3fucosyltransferases in cystic fibrosis airway epithelial cells Biochimie 85 2003 363-367
7. Rhim A.D. Head S. Glick M.C. Scanlin T.F. Possible mechanism of altered sialylation in CF airway epithelial cells Pediatr. Pulmonol. Suppl 25 2003 2401
8. Rhim A.D. Stoykova L. Glick M.C. Scanlin T.F. Terminal glycosylation in cystic fibrosis (CF): A review emphasizing the airway epithelial cell Glycoconj. J. 18 2001 649-659
9. Mitchell E. Houles C. Sudakevitz D. Wimmerova M. Gautier C. Perez S et al. Structural basis for oligosaccharide-mediated adhesion of Pseudomonas aeruginosa in the lungs of cystic fibrosis patients Nat. Struct. Biol. 9 2002 918-921