The bronchopulmonary pathology of alpha-1 antitrypsin (AAT) deficiency: Findings of the Death Review Committee of the national registry for individuals with severe deficiency of alpha-1 antitrypsin

Human Pathology

Volumn 35, Issue 12, 2004, Pages 1452-1461

  Tomashefski Jr , Joseph F ^a,b,c,d,e   Crystal, Ronald G ^a,b,c,d   Wiedemann, Herbert P ^a,b,c,d   Mascha, Edward ^a,b,c,d   Stoller, James K ^a,b,c,d  

^a METROHEALTH MEDICAL CENTER   (United States)

^b WEILL CORNELL MEDICAL CENTER   (United States)

^c Dept of Pulmon Critical Care Med ^*  (United States)

^d LERNER RESEARCH INSTITUTE   (United States)

^e 44109 1998 ^*  (United States)

Author keywords

AAT; alpha 1 antitrypsin deficiency; alpha 1 antitrypsin; bronchiectasis; chronic bronchitis; chronic obstructive pulmonary diease; COPD; diffusing capacity of the lungs for carbon monoxide; DLco; DRC; emphysema; pulmonary pathology

Indexed keywords

ALPHA 1 ANTITRYPSIN;

ADULT; ALPHA 1 ANTITRYPSIN DEFICIENCY; BRONCHIECTASIS; BRONCHIOLE; CAUSE OF DEATH; CHRONIC BRONCHITIS; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; CORRELATION ANALYSIS; CORRELATION FUNCTION; DISEASE SEVERITY; EMPHYSEMA; FEMALE; GOBLET CELL; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; HYPERPLASIA; INFLAMMATION; LIVER DISEASE; LIVER FIBROSIS; LUNG DISEASE; LUNG FUNCTION; MALE; REVIEW; SMALL AIRWAY DISEASE;

EID: 10944232402     PISSN: 00468177     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.humpath.2004.08.013     Document Type: Article

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