Treatment of Panniculitis Associated with Alpha-1-Antitrypsin Deficiency with Alpha-1-Protease Inhibitor

Acta Dermato-Venereologica

Volumn 83, Issue 6, 2003, Pages 462-463

  Kjus, Trine ^a   Lützow Holm, Claus ^a   Christensen, Ole B ^a  

^a ULLEVÅL UNIVERSITY HOSPITAL   (Norway)

Author keywords

[No Author keywords available]

Indexed keywords

ALPHA 1 ANTITRYPSIN; DAPSONE; DOXYCYCLINE; HEMOGLOBIN; PREDNISOLONE;

ADULT; ALPHA 1 ANTITRYPSIN DEFICIENCY; ANAMNESIS; BACTERIAL GROWTH; CASE REPORT; CELL INFILTRATION; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INGUINAL REGION; LABORATORY TEST; LETTER; LEUKOCYTE; NEWBORN HEPATITIS; PANNICULITIS; POLYMORPHONUCLEAR CELL; PRIORITY JOURNAL; SCAR FORMATION; SIDE EFFECT; SKIN EXAMINATION; TACHYCARDIA; ULCER; VERTIGO;

ADULT; ALPHA 1-ANTITRYPSIN; ALPHA 1-ANTITRYPSIN DEFICIENCY; DOSE-RESPONSE RELATIONSHIP, DRUG; DRUG ADMINISTRATION SCHEDULE; FEMALE; FOLLOW-UP STUDIES; HUMANS; INFUSIONS, INTRAVENOUS; PANNICULITIS, NODULAR NONSUPPURATIVE; RISK ASSESSMENT; SEVERITY OF ILLNESS INDEX; TREATMENT OUTCOME;

EID: 10744233228     PISSN: 00015555     EISSN: None     Source Type: Journal    
DOI: 10.1080/00015550310015004     Document Type: Letter

References (5)

1. Warter J, Storck D, Grosshans E, Metais P, Kuntz, Klumpp T. Syndrome de Weber-Christian associe a un deficit en alpha-1-antitrypsine. Enquete familial. Ann Med Interne (Paris) 1972; 123: 877-882.
2. Smith KC, Su WPD, Pittelkow MR, Winkelmann RK. Clinical and pathologic correlations in 96 patients with panniculitis, including 15 patients with deficient levels of α-1-antitrypsin. J Am Acad Dermatol 1989; 21: 1192-1196.
3. Hendrick SJ, Silverman AK, Solomon AR, Headington JT. α-1-Antitrypsin deficiency associated with panniculitis. J Am Acad Dermatol 1988; 18: 684-692.
4. Humbert P, Faivre B, Gibey R, Agache P. Use of anticollagenase properties of doxycycline in treatment of a-1-antitrypsin deficiency panniculitis. Acta Derm Venereol 1991; 71: 189-194.
5. Dowd SK, Rodgers GC, Callen JP. Effective treatment with α-1-protease inhibitor of chronic cutaneous vasculitis associated with α-1-antitrypsin deficiency. J Am Acad Dermatol 1995; 33: 913-916.