Isovaleric acidaemia: Cranial CT and MRI findings

Pediatric Radiology

Volumn 34, Issue 2, 2004, Pages 160-162

  Sogut, Ayhan ^a   Acun, Ceyda ^a   Aydin, Kubilay ^b   Tomsac, Nazan ^a   Demirel, Fatma ^a   Aktuglu, Cigdem ^c  

^a ZONGULDAK KARAELMAS UNIVERSITY   (Turkey)

^b ISTANBUL UNIVERSITY   (Turkey)

^c ISTANBUL UNIVERSITY   (Turkey)

Author keywords

Brain; Child; CT; Isovaleric acidaemia; Metabolic disorder; MRI

Indexed keywords

CARNITINE; ELECTROLYTE; INSULIN; ISOVALERIC ACID;

ACIDEMIA; ACUTE GASTROENTERITIS; ARTICLE; BRAIN DISEASE; BRAIN SCINTISCANNING; CASE REPORT; CHRONIC DISEASE; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; DEHYDRATION; DIABETIC KETOACIDOSIS; DIAGNOSTIC IMAGING; DIET SUPPLEMENTATION; DIFFERENTIAL DIAGNOSIS; FEMALE; FLUID THERAPY; GLOBUS PALLIDUS; GLUCOSURIA; HUMAN; HYPERGLYCEMIA; HYPERPNEA; IMAGE ANALYSIS; INBORN ERROR OF METABOLISM; IRRITABILITY; KETONURIA; LETHARGY; MESENCEPHALON; METABOLIC ACIDOSIS; MUSCLE CONTRACTION; NUCLEAR MAGNETIC RESONANCE IMAGING; PRESCHOOL CHILD; PRIORITY JOURNAL; PROTEIN RESTRICTION; PYRAMIDAL TRACT; TACHYPNEA; URINALYSIS; VOMITING;

AMINO ACID METABOLISM, INBORN ERRORS; BRAIN; FEMALE; HUMANS; INFANT; ISOVALERYL-COA DEHYDROGENASE; LEUCINE; MAGNETIC RESONANCE IMAGING; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; PENTANOIC ACIDS; TOMOGRAPHY, X-RAY COMPUTED;

EID: 1042303630     PISSN: 03010449     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00247-003-1049-8     Document Type: Article

References (11)

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