Complications associated with heterotaxy syndrome in fontan patients

Pediatric Cardiac Surgery Annual

Volumn 5, Issue 1, 2002, Pages 25-35

  Jacobs, Marshall L ^a,b  

^a ST CHRISTOPHER'S HOSPITAL FOR CHILDREN   (United States)

^b DREXEL UNIVERSITY COLLEGE OF MEDICINE   (United States)

Author keywords

Fontan; Heterotaxy syndrome

Indexed keywords

ARTICLE; BLOOD VOLUME; CYANOSIS; FONTAN PROCEDURE; HEART MUSCLE CONDUCTION SYSTEM; HEART SINGLE VENTRICLE; HETEROTAXY SYNDROME; HIGH RISK PATIENT; HUMAN; LUNG ARTERIOVENOUS SHUNT; LUNG BLOOD FLOW; LUNG CIRCULATION; NEWBORN; NEWBORN PERIOD; OUTCOMES RESEARCH; PALLIATIVE THERAPY; PULMONARY VEIN; PULMONARY VEIN OBSTRUCTION; RISK REDUCTION; SINUS NODE; SURGICAL PATIENT; SURGICAL RISK; SURGICAL TECHNIQUE; SURVIVAL TIME; SYSTEMIC CIRCULATION; VENOUS RETURN;

EID: 1042298567     PISSN: 10929126     EISSN: None     Source Type: Journal    
DOI: 10.1053/pcsu.2002.31500     Document Type: Article

References (34)

1. Becker AE, Anderson RH: Pathology of Congenital Heart Disease. London, Butterworths, 1981
2. Van Mierop LHS, Wiglesworth FW: Isomerism of the cardiac atria in the asplenia syndrome. Lab Invest 11: 1303-1315, 1962
3. Moller JH, Nakib A, Anderson RC, et al: Congenital cardiac disease associated with polysplenia. A developmental complex of bilateral "left-sidedness." Circulation 36:789-799, 1967
4. Jacobs ML, Mayer JE Jr: Congenital Heart Surgery Nomenclature and Database Project: Single ventricle. Ann Thorac Surg 69:S197-S204, 2000 (suppl)
5. Van Praagh S, Santini F, Sanders SP: Cardiac malpositions with special emphasis on visceral heterotaxy (asplenia and polysplenia syndromes), in Fyler DC (ed): Nadas' Pediatric Cardiology. Philadelphia, PA, Hanley & Belfus, 1992, pp 589-608
6. Rubino M, Van Praagh S, Kadoba K, et al: Systemic and pulmonary venous connections in visceral heterotaxy with asplenia. Diagnostic and surgical considerations based on seventy-two autopsied cases. J Thorac Cardiovasc Surg 110:641-650, 1995
7. Peoples WM, Moller JH, Edwards JE: Polysplenia: A review of 146 cases. Pediatr Cardiol 4:129-137, 1983
8. Ho SY, Seo JW, Brown NA, et al: Morphology of the sinus node in human and mouse hearts with isomerism of the atrial appendages. Br Heart J 74:437-442, 1995
9. Gaynor JW, Collins MH, Rychik J, et al: Long-term outcome of infants with single ventricle and total anomalous pulmonary venous connection. J Thorac Cardiovasc Surg 117:506-513, 1999
10. Heinemann MK, Hanley FL, Van Praagh S, et al: Total anomalous pulmonary venous drainage in newborns with visceral heterotaxy. Ann Thorac Surg 57:88-91, 1994
11. Sadiq M, Stumper O, De Giovanni JV, et al: Management and outcome of infants and children with right atrial isomerism. Heart 75:314-319, 1996
12. Hashmi A, Abu-Sulaiman R, McCrindle BW, et al: Management and outcomes of right atrial isomerism: A 26-year experience. J Am Coll Cardiol 31:1120-1126, 1998
13. McElhinney DB, Reddy VM, Moore P, et al: Bidirectional cavopulmonary shunt in patients with anomalies of systemic and pulmonary venous drainage. Ann Thorac Surg 63:1676-1684, 1997
14. Alejos JC, Williams RG, Jarmakani JM, et al: Factors influencing survival in patients undergoing the bidirectional Glenn anastomosis. Am J Cardiol 75:1048-1050, 1995
15. Gentles TL, Mayer JE Jr, Gauvreau K, et al: Fontan operation in five hundred consecutive patients: Factors influencing early and late outcome. J Thorac Cardiovasc Surg 114:376-391, 1997
16. Culbertson CB, George BL, Day RW, et al: Factors influencing survival of patients with heterotaxy syndrome undergoing the Fontan procedure. J Am Coll Cardiol 20: 678-684, 1992
17. Cetta F, Feldt RH, O'Leary PW, et al: Improved early morbidity and mortality after Fontan operation: The Mayo Clinic experience, 1987 to 1992. J Am Coll Cardiol 28:480-486, 1996
18. Mainwaring RD, Lamberti JJ: Extracardiac conduit Fontan for children with heterotaxy and functionally single ventricle. Cardiol Young 8:479-485, 1998
19. Stamm C, Friehs I, Mayer JE Jr, et al: Long-term results of the lateral tunnel Fontan operation. J Thorac Cardiovasc Surg 121:28-41, 2001
20. Kawashima Y, Kitamura S, Matsuda H, et al: Total cavopulmonary shunt operation in complex cardiac anomalies. A new operation. J Thorac Cardiovasc Surg 87:74-81, 1984
21. Shah MJ, Rychik J, Fogel MA, et al: Pulmonary AV malformations after superior cavopulmonary connection: Resolution after inclusion of hepatic veins in the pulmonary circulation. Ann Thorac Surg 63:960-963, 1997
22. Knight WB, Mee RBBB: A cure for pulmonary arteriovenous fistulas? Ann Thorac Surg 59:999-1001, 1995
23. Papagiannis J, Kanter RJ, Effman EL, et al: Polysplenia with pulmonary arteriovenous malformations. Pediatr Cardiol 14:127-129, 1993
24. Kapur S, Rome J, Chandra RS: Diffuse pulmonary arteriovenous malformation in a child with polysplenia syndrome. Pediatr Pathol Lab Med 15:463-468, 1995
25. Bernstein HS, Brook MM, Silverman NH, et al: Development of pulmonary arteriovenous fistulae in children after cavopulmonary shunt. Circulation 92:II-309-II-314, 1995 (suppl 9)
26. Chang RK, Alejos JC, Atkinson D, et al: Bubble contrast echocardiography in detecting pulmonary arteriovenous shunting in children with univentricular heart after cavopulmonary anastomosis. J Am Coll Cardiol 33:2052-2058, 1999
27. Jacobs ML, Pourmoghadam KK, Geary EM, et al: Pulmonary arteriovenous malformations after cavopulmonary connection. Ann Thorac Surg 69:634-635, 2000
28. Srivastava D, Preminger T, Lock JE, et al: Hepatic venous blood and the development of pulmonary arteriovenous malformations in congenital heart disease. Circulation 92:1217-1222, 1995
29. Duncan BW, Kneebone JM, Chi EY, et al: A detailed histologic analysis of pulmonary arteriovenous malformations in children with cyanotic congenital heart disease. J Thorac Cardiovasc Surg 117:931-938, 1999
30. Starnes SL, Duncan BW, Kneebone JM, et al: Pulmonary microvessel density is a marker of angiogenesis in children after cavopulmonary anastomosis. J Thorac Cardiovasc Surg 120:902-907, 2000
31. Malhotra SP, Riemer RK, Thelitz S, et al: Superior cavopulmonary anastomosis suppresses the activity and expression of pulmonary angiotensin-converting enzyme. J Thorac Cardiovasc Surg 122:464-469, 2001
32. Hishitani T, Ogawa K, Hoshino K, et al: Surgical ligation of anomalous hepatic vein in a case of heterotaxy syndrome with massive intrahepatic shunting after modified Fontan operation. Pediatr Cardiol 20:428-430, 1999
33. Slavik Z, Lamb RK, Webber SA, et al: A rare cause of profound cyanosis after Kawashima modification of bidirectional cavopulmonary anastomosis. Ann Thorac Surg 60:435-437, 1995
34. Uemura H, Yagihara T, Hattori R, et al: Redirection of hepatic venous drainage after total cavopulmonary shunt in left isomerism. Ann Thorac Surg 68:1731-1735, 1999