Short-chain 3-hydroxyacyl-CoA dehydrogenase deficiency associated with hyperinsulinism: A novel glucose-fatty acid cycle?

Biochemical Society Transactions

Volumn 31, Issue 6, 2003, Pages 1137-1139

  Eaton, S ^a   Chatziandreou, I ^a   Krywawych, S ^a   Pen, S ^a   Clayton, P T ^a   Hussain, K ^a  

^a UNIVERSITY COLLEGE LONDON   (United Kingdom)

Author keywords

3 hydroxyacyl CoA dehydrogenase; Carnitine palmitoyltransferase I (CPT I); Hyperinsulinism; oxidation

Indexed keywords

3 HYDROXYACYL COENZYME A DEHYDROGENASE; CARNITINE PALMITOYLTRANSFERASE; FATTY ACID; GLUCOKINASE; GLUCOSE; GLUTAMATE DEHYDROGENASE; INSULIN; SHORT CHAIN 3 HYDROXYACYL COENZYME A DEHYDROGENASE; SHORT CHAIN FATTY ACID; UNCLASSIFIED DRUG;

CONFERENCE PAPER; ENZYME DEFICIENCY; FATTY ACID METABOLISM; FATTY ACID OXIDATION; GLUCOSE BLOOD LEVEL; GLUCOSE FATTY ACID CYCLE; GLUCOSE METABOLISM; HYPERINSULINISM; HYPERINSULINISM OF INFANCY; INSULIN RELEASE; K ATP CHANNELOPATHY; PANCREAS ISLET BETA CELL; PRIORITY JOURNAL; SHORT CHAIN 3 HYDROXYACYL COENZYME A DEHYDROGENASE DEFICIENCY;

EID: 0346788907     PISSN: 03005127     EISSN: None     Source Type: Journal    
DOI: 10.1042/bst0311137     Document Type: Conference Paper

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