Galactitol and galactonate accumulation in heart and skeletal muscle of mice with deficiency of galactose-1-phosphate uridyltransferase

Molecular Genetics and Metabolism

Volumn 81, Issue 2, 2004, Pages 105-111

  Yager, Claire ^a   Ning, Cong ^a,c   Reynolds, Robert ^a   Leslie, Nancy ^b   Segal, Stanton ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

^b CINCINNATI CHILDREN S HOSPITAL RESEARCH FOUNDATION   (United States)

^c EUNICE KENNEDY SHRIVER NATIONAL INSTITUTE OF CHILD HEALTH AND HUMAN DEVELOPMENT   (United States)

Author keywords

Galactitol; Galactonate; Galactosemic mice; Heart; Muscle

Indexed keywords

GALACTITOL; GALACTONIC ACID; GALACTOSE 1 PHOSPHATE URIDYLYLTRANSFERASE; GLUCOSE DERIVATIVE; UNCLASSIFIED DRUG;

ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BRAIN; CONTROLLED STUDY; ENZYME ACTIVITY; GALACTOSEMIA; GLUCOSE INTAKE; GLUCOSE METABOLISM; GLUCOSE OXIDATION; GLUCOSE URINE LEVEL; HEART MUSCLE; KIDNEY; LIVER; MOUSE; NONHUMAN; PRIORITY JOURNAL; SKELETAL MUSCLE; SUCKLING; TISSUE DISTRIBUTION;

ANIMALIA;

EID: 0346040220     PISSN: 10967192     EISSN: None     Source Type: Journal    
DOI: 10.1016/j.ymgme.2003.10.001     Document Type: Article

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