Adult glycogenosis II with paracrystalline mitochondrial inclusions and Hirano bodies in skeletal muscle

Neuromuscular Disorders

Volumn 9, Issue 3, 1999, Pages 136-143

  Fernández, Roberto ^a   Fernández, José M ^b   Cervera, Carlos ^c   Teijeira, Susana ^a   Teijeiro, Alfonso ^a   Domínguez, Carmen ^c   Navarro, Carmen ^a  

^a HOSPITAL DO MEIXOEIRO   (Spain)

^b HOSPITAL XERAL CÍES   (Spain)

^c HOSPITAL UNIVERSITARI VALL D HEBRON   (Spain)

Author keywords

Acid maltase; Glycogenosis II; Hirano bodies; Paracrystalline mitochondrial inclusions; Skeletal muscle

Indexed keywords

GLUCAN 1,4 ALPHA GLUCOSIDASE;

ADULT; ARTICLE; CASE REPORT; CELL INCLUSION; ELECTRON MICROSCOPY; ENZYME DEFICIENCY; FEMALE; FIBROBLAST; GLYCOGEN STORAGE DISEASE TYPE 2; HISTOPATHOLOGY; HUMAN; HUMAN CELL; HUMAN TISSUE; MITOCHONDRION; MUSCLE BIOPSY; NEUROPHYSIOLOGY; PRIORITY JOURNAL; SKELETAL MUSCLE; ULTRASTRUCTURE;

FEMALE; FIBROBLASTS; GLYCOGEN STORAGE DISEASE TYPE II; HUMANS; INCLUSION BODIES; LYSOSOMES; MICROSCOPY, ELECTRON; MIDDLE AGED; MITOCHONDRIA; MUSCLE, SKELETAL; SKIN;

EID: 0345104424     PISSN: 09608966     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0960-8966(98)00117-5     Document Type: Article

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