Biochemistry of glutaric aciduria type I: Activities of in vitro expressed wild-type and mutant cDNA encoding human glutaryl-CoA dehydrogenase

Journal of Inherited Metabolic Disease

Volumn 22, Issue 3, 1999, Pages 256-258

  Liesert, M ^a   Zschocke, J ^b   Hoffmann, G F ^b   Muhlhauser N ^a   Buckel, W ^a  

^a PHILIPPS UNIVERSITY MARBURG   (Germany)

^b University Children's Hospital   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

COMPLEMENTARY DNA; DICARBOXYLIC ACID; GLUTARIC ACID; GLUTARYL COENZYME A DEHYDROGENASE; HYDROXYLYSINE; LYSINE; OXIDOREDUCTASE; TRYPTOPHAN;

ACIDURIA; BIOCHEMISTRY; CATABOLISM; CONFERENCE PAPER; DECARBOXYLATION; ENZYME ACTIVITY; ESCHERICHIA COLI; HUMAN; IN VITRO STUDY; MUTANT; NONHUMAN; OXIDATION; PATHOGENESIS;

ESCHERICHIA COLI; GENE EXPRESSION; GLUTARATES; GLUTARYL-COA DEHYDROGENASE; HUMANS; MUTAGENESIS; OXIDOREDUCTASES; OXIDOREDUCTASES ACTING ON CH-CH GROUP DONORS; RECOMBINANT PROTEINS;

EID: 0345086480     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1005525903207     Document Type: Conference Paper

References (9)

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