Restoration of hepatic cytochrome c oxidase activity and expression with acetyl-L-carnitine treatment in spf mice with an ornithine transcarbamylase deficiency

Biochemical Pharmacology

Volumn 55, Issue 11, 1998, Pages 1853-1860

  Mawal, Yogesh R ^a   Rama Rao, K V ^a   Qureshi, Ijaz A ^a  

^a UNIVERSITY OF MONTREAL   (Canada)

Author keywords

Acetyl L carnitine; Congenital hyperammonemia; Cytochrome c oxidase; Liver mitochondria; Ornithine transcarbamylase; Spf mice

Indexed keywords

ADENOSINE TRIPHOSPHATE; AMMONIA; CHOLESTEROL; CYTOCHROME C OXIDASE; LEVACECARNINE; MESSENGER RNA; ORNITHINE CARBAMOYLTRANSFERASE; PHOSPHOLIPID;

ANIMAL CELL; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELL LEVEL; DRUG MECHANISM; ENZYME ACTIVITY; ENZYME DEFICIENCY; HYPERAMMONEMIA; LIVER LEVEL; MOUSE; MUTANT; NONHUMAN; NORTHERN BLOTTING; PRIORITY JOURNAL; PROTEIN EXPRESSION;

ACETYLCARNITINE; AMINO ACID METABOLISM, INBORN ERRORS; AMMONIA; ANIMALS; CARBAMOYL-PHOSPHATE SYNTHASE (AMMONIA); CHOLESTEROL; ELECTRON TRANSPORT COMPLEX IV; ENERGY METABOLISM; ENZYME INDUCTION; INTRACELLULAR MEMBRANES; ISOENZYMES; MALE; MICE; MITOCHONDRIA, LIVER; ORNITHINE CARBAMOYLTRANSFERASE; PHOSPHOLIPIDS; RNA, MESSENGER;

EID: 0344157873     PISSN: 00062952     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0006-2952(98)00051-3     Document Type: Article

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