Congenital erythropoietic porphyria: Dilemmas in present day management

Clinical and Experimental Dermatology

Volumn 27, Issue 8, 2002, Pages 680-683

  Dawe, Simon A ^a   Stephens, A D ^a   Peters, T J ^a   Du Vivier, A ^a   Creamer, J D ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

CAROTENE; CHARCOAL; COPROPORPHYRIN; HEMOGLOBIN; UROPORPHYRIN; UROPORPHYRINOGEN III SYNTHASE;

ADULT; ALLOGENIC BONE MARROW TRANSPLANTATION; ARTICLE; BACTERIAL INFECTION; BLOOD TRANSFUSION; BONE MARROW DISEASE; BONE MARROW HYPERPLASIA; CASE REPORT; CLINICAL FEATURE; CONGENITAL ERYTHROPOIETIC PORPHYRIA; HEMATOCRIT; HEMATOLOGIC DISEASE; HEMOLYTIC ANEMIA; HUMAN; IRON OVERLOAD; LABORATORY TEST; MALE; MORTALITY; PHOTOSENSITIVITY DISORDER; PRIORITY JOURNAL; SCAR FORMATION; SPLENECTOMY; SPLENOMEGALY; STAPHYLOCOCCUS AUREUS; TREATMENT OUTCOME;

ADULT; ANEMIA, HEMOLYTIC; BLOOD TRANSFUSION; BONE DISEASES; DEFEROXAMINE; FEMALE; HEMATOPOIETIC STEM CELL TRANSPLANTATION; HUMANS; IRON CHELATING AGENTS; IRON OVERLOAD; PORPHYRIA, ERYTHROPOIETIC;

EID: 0242684753     PISSN: 03076938     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2230.2002.01166.x     Document Type: Article

References (10)

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