Familial urticaria pigmentosa associated with thrombocytosis as the initial symptom of systemic mastocytosis and Down's syndrome

Journal of the European Academy of Dermatology and Venereology

Volumn 17, Issue 6, 2003, Pages 718-722

  Jappe, Uta ^a,b   Aumann, V ^a   Mittler, U ^a   Gollnick, H ^a  

^a OTTO VON GUERICKE UNIVERSITY   (Germany)

^b UNIVERSITY OF HEIDELBERG   (Germany)

Author keywords

Down's syndrome; Familial urticaria pigmentosa; Mastocytosis; Thrombocytosis; Trisomy 21

Indexed keywords

ARTICLE; ASTHMA; CASE REPORT; DIARRHEA; DISEASE ASSOCIATION; DISEASE COURSE; DOWN SYNDROME; FAMILIAL DISEASE; GENETIC ASSOCIATION; GENETIC PREDISPOSITION; GENETICS; HEPATOMEGALY; HISTOPATHOLOGY; HOSPITALIZATION; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MALE; MASTOCYTOSIS; NEEDLE BIOPSY; PRESCHOOL CHILD; PRIORITY JOURNAL; PROGNOSIS; RISK ASSESSMENT; SIBLING; SPLENOMEGALY; THROMBOCYTOSIS; TRISOMY 21; URTICARIA PIGMENTOSA;

BIOPSY, NEEDLE; CHILD, PRESCHOOL; DOWN SYNDROME; GENETIC PREDISPOSITION TO DISEASE; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; MASTOCYTOSIS; PROGNOSIS; RISK ASSESSMENT; SEVERITY OF ILLNESS INDEX; SIBLINGS; THROMBOCYTOSIS; URTICARIA PIGMENTOSA;

EID: 0242539749     PISSN: 09269959     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1468-3083.2003.00834.x     Document Type: Article

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