Stereoselective analysis of 2-hydroxysebacic acid in urine of patients with Zellweger syndrome and of premature infants fed with medium-chain triglycerides

Journal of Inherited Metabolic Disease

Volumn 26, Issue 6, 2003, Pages 583-592

  Muth, A ^a   Mosandl, A ^a   Wanders, R J A ^b   Nowaczyk, M J M ^c   Baric, I ^d   Bohles H ^a   Sewell, A C ^a,e  

^a GOETHE UNIVERSITY   (Germany)

^b UNIVERSITY OF AMSTERDAM   (Netherlands)

^c MCMASTER UNIVERSITY   (Canada)

^d KBC Zagreb   (Croatia)

^e UNIVERSITY HOSPITAL FRANKFURT   (Germany)

Author keywords

[No Author keywords available]

Indexed keywords

2 HYDROXYSEBACIC ACID; MEDIUM CHAIN TRIACYLGLYCEROL; SEBACIC ACID; UNCLASSIFIED DRUG;

ARTICLE; CLINICAL ARTICLE; CONTROLLED STUDY; ENANTIOSELECTIVITY; FATTY ACID ANALYSIS; FATTY ACID OXIDATION; GAS CHROMATOGRAPHY; HUMAN; INFANT; INFANT FEEDING; MASS SPECTROMETRY; METABOLITE; PREMATURITY; STEREOCHEMISTRY; URINALYSIS; URINARY EXCRETION; ZELLWEGER SYNDROME;

CHILD, PRESCHOOL; CHROMATOGRAPHY, GAS; DECANOIC ACIDS; DIET; FEMALE; HUMANS; HYDROXY ACIDS; INFANT; INFANT, NEWBORN; INFANT, PREMATURE; MALE; MASS SPECTROMETRY; STEREOISOMERISM; TRIGLYCERIDES; ZELLWEGER SYNDROME;

EID: 0142182123     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1025908216639     Document Type: Article

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