Rasmussen's syndrome

Neurological Sciences

Volumn 24, Issue SUPPL. 4, 2003, Pages

  Granata, T ^a  

^a DEPARTMENT OF NEUROSURGERY   (Italy)

Author keywords

Autoimmunity; Epilepsy; Immunoglobulin; Immunomodulation

Indexed keywords

AUTOANTIBODY; AZATHIOPRINE; CORTICOSTEROID; CORTICOTROPIN; CYCLOPHOSPHAMIDE; DEXAMETHASONE; GLUTAMATE RECEPTOR; IMMUNOGLOBULIN; IMMUNOMODULATING AGENT; IMMUNOSUPPRESSIVE AGENT; METHYLPREDNISOLONE; PREDNISONE; STEROID;

ADOLESCENT; ADULT; ANTIBODY BLOOD LEVEL; ARTICLE; AUTOIMMUNE DISEASE; BRAIN ATROPHY; CHILD; CLINICAL FEATURE; CLINICAL TRIAL; DIAGNOSTIC IMAGING; DISEASE ASSOCIATION; DISEASE COURSE; DOSE RESPONSE; DRUG EFFICACY; DRUG MEGADOSE; FEMALE; FOCAL EPILEPSY; HUMAN; IMMUNOHISTOCHEMISTRY; IMMUNOMODULATION; IMMUNOPATHOGENESIS; INFANT; LABORATORY TEST; MALE; MENTAL DETERIORATION; NEUROPATHOLOGY; PLASMAPHERESIS; RASMUSSEN SYNDROME;

ANIMALS; AUTOANTIBODIES; DISEASE MODELS, ANIMAL; ENCEPHALITIS; HUMANS; IMMUNOGLOBULINS, INTRAVENOUS; RECEPTORS, AMPA;

EID: 0142155237     PISSN: 15901874     EISSN: None     Source Type: Journal    
DOI: 10.1007/s10072-003-0086-2     Document Type: Article

References (22)

1. Dulac O (1996) Rasmussen's syndrome. Curr Opin Neurol 9:75-77
2. Bien CG, Widman G, Urbach H et al (2002) The natural history of Rasmussen's encephalitis. Brain 125:1751-1759
3. Rogers SW, Andrews PI, Gahring LC et al (1994) Autoantibodies to glutamate receptor GluR3 in Rasmussen's encephalitis. Science 265:648-651
4. Twiman RE, Gahring LC, Spless C, Rogers SW (1995) Glutamate receptor antibodies activate a subset of receptors and reveal an agonist binding site. Neuron 14:755-762
5. He XP, Patel M, Whitney KD, Janumpalli S, Tenner A, McNamara JO (1998) Glutamate receptor GluR3 antibodies and death of cortical cells. Neuron 20:153-163
6. Levite M, Fleidervish IA, Schwarz A et al (1999) Autoantibodies to the glutamate receptor kill neurons via activation of receptor ion channel. J Autoimmun 13:61-72
7. Whitney KD, Andrews PI, McNamara JO (1999) Immunoglobulin G and complement immunoreactivity in the cerebral cortex of patients with Rasmussen's encephalitis. Neurology 53:699-708
8. Frassoni C, Spreafico R, Franceschetti S et al (2001) Labeling of rat neurons by anti-GluR3 IgG from patients with Rasmussen's encephalitis. Neurology 57:324-327
9. Hart YM, Andermann F, Fish DR et al (1997) Chronic encephalitis and epilepsy in adults and adolescents: a variant of Rasmussen's syndrome? Neurology 48:418-424
10. Granata T, Spreafico R, Gobbi G et al (2003) Rasmussen's encephalitis: early characteristics allow diagnosis. Neurology 60:422-425
11. Leach JP, Chadwick DW, Miles JB, Hart IK (1999) Improvement in adult-onset Rasmussen's encephalitis with long-term immunomodulatory therapy. Neurology 52:738-742
12. Villani F, Spreafico R, Farina L et al (2001) Positive response to immunomodulatory therapy in an adult patient with Rasmussen's encephalitis. Neurology 56:248-250
13. Chiapparini L, Granata T, Farina L et al (2003) Diagnostic imaging in 13 cases of Rasmussen's encephalitis: can early MRI suggest the diagnosis? Neuroradiology 45:171-183
14. Andrews JM, Thompson JA, Pysher TJ, Walker ML, Hammond ME (1990) Chronic encephalitis, epilepsy, and cerebrovascular immune complex deposits. Ann Neurol 28:88-90
15. Krauss GL, Campbell ML, Roche KW, Huganir RL, Niedermeyer E (1996) Chronic steroid-responsive encephalitis without autoantibodies to glutamate receptor GluR3. Neurology 46:247-249
16. Mantegazza R, Bernasconi P, Baggi F et al (2002) Antibodies against GluR3 peptides are not specific for Rasmussen's encephalitis but are also present in epilepsy patients with severe, early onset disease and intractable seizures. J Neuroimmunol 131:179-185
17. Chinchilla D, Dulac O, Robain O et al (1994) Reappraisal of Rasmussen's syndrome with special emphasis on treatment with high doses of steroids. J Neurol Neurosurg Psychiatry 57:1325-1333
18. Hart YM, Cortez M, Andermann F et al (1994) Medical treatment of Rasmussen's syndrome (chronic encephalitis and epilepsy): effect of high-dose steroids or immunoglobulins in 19 patients. Neurology 44:1030-1036
19. Andrews PI, Dichter MA, Berkovic SF, Newton MR, McNamara JO (1996) Plasmapheresis in Rasmussen's encephalitis. Neurology 46:242-246
20. Antozzi C, Granata T, Aurisano N et al (1998) Long-term selective IgG immunoadsorption improves Rasmussen's encephalitis. Neurology 51:302-305
21. Walsh PJ (1991) Treatment of Rasmussen's syndrome with intravenous gammaglobulin. In: Andermann F (ed) Chronic encephalitis and epilepsy. Rasmussen's syndrome. Butterworth-Heinemann, Boston, pp 201-204
22. Wise MS, Rutledge SL, Kuzniecky RI (1996) Rasmussen's syndrome and long-term response to gamma globulin. Ped Neurol 14:149-152