Lupus-like panniculitis in a patient with autoimmune polyendocrinopathy-candidiasis-ectodermal dystrophy (APECED)

Experimental and Clinical Endocrinology and Diabetes

Volumn 111, Issue 5, 2003, Pages 288-293

  Füchtenbuschl, Martin ^a   Vogel, A ^b   Achenbach, P ^a   Gummer, M ^a   Ziegler, A G ^a   Albert, E ^c   Standl, E ^a   Manns, M P ^b  

^a Klinikum Schwabing   (Germany)

^b HANNOVER MEDICAL SCHOOL   (Germany)

^c UNIVERSITY OF MUNICH   (Germany)

Author keywords

AIRE; APECED; Autoimmune; HLA; Panniculitis

Indexed keywords

CORTICOSTEROID; IMMUNOGLOBULIN BINDING FACTOR;

ADRENAL CORTEX INSUFFICIENCY; ADULT; ARTICLE; AUTOIMMUNE DISEASE; AUTOIMMUNE POLYENDOCRINOPATHY CANDIDIASIS ECTODERMAL DYSTROPHY; AUTOSOMAL RECESSIVE DISORDER; CANDIDIASIS; CASE REPORT; CLINICAL FEATURE; CODON; COMPLEMENT FACTOR; COMPLEMENT FIXATION; CORTICOSTEROID THERAPY; DIABETIC COMA; DISEASE ASSOCIATION; DNA SEQUENCE; ECTODERMAL DYSPLASIA; ENTEROBACTER CLOACAE; ENZYME LINKED IMMUNOSORBENT ASSAY; EXON; FEMALE; GENE MUTATION; HAPLOTYPE; HISTOPATHOLOGY; HLA TYPING; HUMAN; HUMAN TISSUE; IMMUNOFLUORESCENCE; IMMUNOHISTOCHEMISTRY; IMMUNOLOGICAL TOLERANCE; IMMUNOREGULATION; IMMUNOSUPPRESSIVE TREATMENT; KETOACIDOSIS; MUTATIONAL ANALYSIS; NONSENSE MUTATION; PANNICULITIS; POLYMERASE CHAIN REACTION; PRIORITY JOURNAL; REGULATOR GENE; REMISSION; SCAR FORMATION; SEPSIS; SEQUENCE ANALYSIS; SKIN BIOPSY; SKIN ULCER; VASCULITIS; WESTERN BLOTTING;

ADULT; AUTOANTIBODIES; BIOPSY; CANDIDIASIS; CODON, NONSENSE; FEMALE; FLUORESCENT ANTIBODY TECHNIQUE; HISTOCOMPATIBILITY TESTING; HUMANS; IMMUNOSUPPRESSIVE AGENTS; MALE; PANNICULITIS, LUPUS ERYTHEMATOSUS; PEDIGREE; POLYENDOCRINOPATHIES, AUTOIMMUNE; SKIN; TRANSCRIPTION FACTORS;

EID: 0042926617     PISSN: 09477349     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2003-41287     Document Type: Article

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