Mice lacking phosphatidylinositol transfer protein-α exhibit spinocerebellar degeneration, intestinal and hepatic steatosis, and hypoglycemia

Journal of Biological Chemistry

Volumn 278, Issue 35, 2003, Pages 33501-33518

  Alb Jr , James G ^a   Cortese, Jorge D ^a   Phillips, Scott E ^a   Albin, Roger L ^b   Nagy, Tim R ^c   Hamilton, Bruce A ^d   Bankaitis, Vytas A ^a  

^a UNIVERSITY OF NORTH CAROLINA   (United States)

^b UNIVERSITY OF MICHIGAN MEDICAL SCHOOL   (United States)

^c UNIVERSITY OF ALABAMA AT BIRMINGHAM   (United States)

^d UNIVERSITY OF CALIFORNIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

FATTY ACIDS; GENES; GLUCOSE; LIPIDS; PROTEINS;

GENE EXPRESSION;

BIOCHEMISTRY;

ADENOSINE DIPHOSPHATE; ADENOSINE TRIPHOSPHATE; CALNEXIN; CARRIER PROTEIN; DIACYLGLYCEROL; FATTY ACID; GLUCOSE; GLYCOGEN; LIPID; PHOSPHATIDYLINOSITOL; PHOSPHATIDYLINOSITOL TRANSFER PROTEIN ALPHA; TRIACYLGLYCEROL; TUNICAMYCIN; UNCLASSIFIED DRUG;

ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CEREBELLUM; DUODENUM; ELECTRON MICROSCOPY; ENDOPLASMIC RETICULUM; ENTEROPATHY; FATTY LIVER; GASTROINTESTINAL DISEASE; GENOTYPE; HYPOGLYCEMIA; INFLAMMATION; INTESTINE BIOPSY; LIPID METABOLISM; LIVER BIOPSY; MOUSE; NEUROLOGIC DISEASE; NONHUMAN; NUCLEOTIDE SEQUENCE; PANCREAS ISLET BETA CELL; PHENOTYPE; PRIORITY JOURNAL; PROTEIN DEFICIENCY; SPINAL CORD BIOPSY; SPINOCEREBELLAR DEGENERATION;

ADENOSINE TRIPHOSPHATE; ANIMALS; BRAIN; CARRIER PROTEINS; CEREBELLUM; DOSE-RESPONSE RELATIONSHIP, DRUG; ENDOPLASMIC RETICULUM; FATTY ACIDS; GENETIC VECTORS; GENOTYPE; GLUCAGON; GLYCOGEN; HYPOGLYCEMIA; IN SITU NICK-END LABELING; INTESTINAL DISEASES; LIPID METABOLISM; LIVER; LIVER DISEASES; MEMBRANE PROTEINS; MICE; MICE, INBRED C57BL; MICE, TRANSGENIC; MICROSCOPY, ELECTRON; MODELS, GENETIC; PHENOTYPE; PHOSPHOLIPID TRANSFER PROTEINS; PROGLUCAGON; PROTEIN PRECURSORS; SACCHAROMYCES CEREVISIAE PROTEINS; SPINOCEREBELLAR DEGENERATIONS; TIME FACTORS;

ANIMALIA; MAMMALIA;

EID: 0042780282     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M303591200     Document Type: Article

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