Cardiomyopathy and pericardial effusion in infancy point to a fatty acid β-oxidation defect after exclusion of an underlying infection

Pediatric Cardiology

Volumn 24, Issue 3, 2003, Pages 295-297

  Spiekerkoetter, U ^a   Tenenbaum, T ^a   Heusch, A ^a   Wendel, U ^a  

^a UNIVERSITY HOSPITAL DÜSSELDORF   (Germany)

Author keywords

Cardiomyopathy; Fatty acid oxidation; Pericardial effusion

Indexed keywords

ACYL COENZYME A DEHYDROGENASE; ACYLCARNITINE; FATTY ACID; MEDIUM CHAIN FATTY ACID; VERY LONG CHAIN FATTY ACID;

ARTICLE; CARDIOMYOPATHY; CASE REPORT; CLINICAL FEATURE; DIET THERAPY; EARLY DIAGNOSIS; ECHOCARDIOGRAPHY; ELECTROCARDIOGRAM; FATTY ACID OXIDATION; FIBROBLAST; GENE MUTATION; GENETIC ANALYSIS; HUMAN; HUMAN CELL; INFANT; INFECTION; PATHOGENESIS; PERICARDIAL EFFUSION; PHENOTYPE; TREATMENT OUTCOME;

ACYL-COA DEHYDROGENASE, LONG-CHAIN; CARDIOMYOPATHIES; ECHOCARDIOGRAPHY; FATTY ACIDS; HUMANS; INFANT; LIPID METABOLISM, INBORN ERRORS; PERICARDIAL EFFUSION; TRIGLYCERIDES;

EID: 0042745435     PISSN: 01720643     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00246-002-0277-2     Document Type: Article

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