Iron metabolism in mice with partial frataxin deficiency

Cerebellum

Volumn 2, Issue 2, 2003, Pages 146-153

  Santos, Manuela M ^a,b   Miranda, Carlos J ^a,b   Levy, Joanne E ^c   Montross, Lynne K ^c   Cossée, Mireille ^d   Sequeiros, Jorge ^b   Andrews, Nancy ^c   Koenig, Michel ^d   Pandolfo, Massimo ^a,e  

^a NOTRE DAME HOSPITAL   (Canada)

^b UNIVERSITY OF PORTO   (Portugal)

^c BOSTON CHILDREN S HOSPITAL   (United States)

^d UNIVERSITY HOSPITAL OF STRASBOURG   (France)

^e ERASME HOSPITAL   (Belgium)

Author keywords

Cardiomyopathy; Frataxin; Friedrich ataxia; Hemochromatosis; Hereditary; Iron overload

Indexed keywords

FRATAXIN; FREE RADICAL; MITOCHONDRIAL PROTEIN; IRON; IRON BINDING PROTEIN;

ALLELE; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUTOSOMAL RECESSIVE INHERITANCE; CARDIOMYOPATHY; CELL RESPIRATION; CELLULAR DISTRIBUTION; CONTROLLED STUDY; DISEASE ASSOCIATION; DISEASE PREDISPOSITION; FRIEDREICH ATAXIA; GENE MUTATION; HEART INJURY; HEART MUSCLE FIBROSIS; HEMOCHROMATOSIS; HOMEOSTASIS; INTRON; IRON INTAKE; IRON METABOLISM; IRON OVERLOAD; IRON STORAGE; KNOCKOUT MOUSE; LETHALITY; MOUSE; NERVE DEGENERATION; NONHUMAN; PHENOTYPE; PRIORITY JOURNAL; WILD TYPE; ANIMAL; DISEASE MODEL; GENETICS; LIVER; METABOLISM; MOUSE MUTANT; PATHOLOGY; REFERENCE VALUE; TRINUCLEOTIDE REPEAT;

ANIMALS; DISEASE MODELS, ANIMAL; FRIEDREICH ATAXIA; HEMOCHROMATOSIS; INTRONS; IRON; IRON-BINDING PROTEINS; LIVER; MICE; MICE, KNOCKOUT; REFERENCE VALUES; TRINUCLEOTIDE REPEATS;

EID: 0042663893     PISSN: 14734222     EISSN: None     Source Type: Journal    
DOI: 10.1080/14734220309408     Document Type: Article

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