Hyperplasia of adrenal rest tissue causing a retroperitoneal mass in a child with 11β-hydroxylase deficiency

Hormone Research

Volumn 60, Issue 2, 2003, Pages 99-102

  Storr, Helen L ^a   Barwick, Tara D ^a   Snodgrass, Graeme A I ^a   Booy, Robert ^a   Morel, Yves ^b   Reznek, Rodney H ^a   Savage, Martin O ^a  

^a ST BARTHOLOMEW S HOSPITAL   (United Kingdom)

^b HÔPITAL DEBROUSSE   (France)

Author keywords

11 Hydroxylase deficiency; Adrenal rest tissue; Congenital adrenal hyperplasia

Indexed keywords

HYDROCORTISONE; STEROID 11BETA MONOOXYGENASE;

ARTICLE; BLOOD; CASE REPORT; CHILD DEVELOPMENT; CLINICAL FEATURE; CONGENITAL ADRENAL HYPERPLASIA; CORTICOSTEROID THERAPY; DISEASE COURSE; DISORDERS OF STEROID METABOLISM; ENZYMOLOGY; GENERAL CONDITION IMPROVEMENT; GENETICS; GONADAL DISEASE; HEMODYNAMIC MONITORING; HUMAN; INBORN ERROR OF METABOLISM; LABORATORY TEST; MALE; MALE GENITAL SYSTEM; METABOLISM; NUCLEAR MAGNETIC RESONANCE IMAGING; PATIENT INFORMATION; PHYSICAL EXAMINATION; PRESCHOOL CHILD; PRIORITY JOURNAL; RETROPERITONEAL DISEASE; RETROPERITONEAL TUMOR; STEROID 11BETA MONOOXYGENASE DEFICIENCY; VIRILIZATION;

ADRENAL HYPERPLASIA, CONGENITAL; CHILD, PRESCHOOL; HUMANS; HYDROCORTISONE; MAGNETIC RESONANCE IMAGING; MALE; METABOLISM, INBORN ERRORS; RETROPERITONEAL NEOPLASMS; STEROID 11-BETA-HYDROXYLASE; VIRILISM;

EID: 0042242693     PISSN: 03010163     EISSN: None     Source Type: Journal    
DOI: 10.1159/000071878     Document Type: Article

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