Presence of an unusual GM2 derivative, taurine-conjugated GM2, in Tay-Sachs brain

Journal of Biological Chemistry

Volumn 278, Issue 37, 2003, Pages 35286-35291

  Li, Yu Teh ^a   Maskos, Karol ^b   Chou, Chau Wen ^c   Cole, Richard B ^c   Li, Su Chen ^a  

^a TULANE UNIVERSITY HEALTH SCIENCES CENTER   (United States)

^b TULANE UNIVERSITY   (United States)

^c UNIVERSITY OF NEW ORLEANS   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BRAIN; DISEASES; MASS SPECTROMETRY; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PATIENT MONITORING; SYNTHESIS (CHEMICAL);

NEURAL DYFUNCTIONS;

BIOCHEMISTRY;

GANGLIOSIDE GM2; TAURINE;

AMIDATION; ARTICLE; CONJUGATION; CONTROLLED STUDY; HUMAN; HUMAN TISSUE; NEUROPATHOLOGY; NUCLEAR MAGNETIC RESONANCE SPECTROSCOPY; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN ANALYSIS; PROTEIN MODIFICATION; TAY SACHS DISEASE;

BRAIN CHEMISTRY; CHROMATOGRAPHY, THIN LAYER; G(M2) GANGLIOSIDE; HUMANS; N-ACETYLNEURAMINIC ACID; SPECTROMETRY, MASS, ELECTROSPRAY IONIZATION; TAURINE; TAY-SACHS DISEASE;

ORYCTOLAGUS CUNICULUS;

EID: 0041315631     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M306126200     Document Type: Article

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