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Quan JM, Tiddens HA, Sy JP, et al.: A two-year randomized, placebo-controlled trial of dornase alfa in young patients with cystic fibrosis with mild lung function abnormalities. J Pediatr 2001, 139:813-820. This study shows that early treatment with dornase alfa can benefit patients with CF with mild lung disease. This provides evidence that early treatment might alter the disease.
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Gappa M, Ranganathan SC, Stocks J: Lung function testing in infants with cystic fibrosis: lessons from the past and future directions. Pediatr Pulmonol 2001, 32:228-245. These authors review infant pulmonary function testing techniques and their value in patients with CF.
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Doull IJ: Recent advances in cystic fibrosis. Arch Dis Child 2001, 85:62-66.
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Orenstein DM, Winnie GB, Altman H: Cystic fibrosis: a 2002 update. J Pediatr 2002, 140:156-164. This article is a superb review of current clinical care for patients with CF.
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