Effect of valproic acid on the urinary metabolic profile of a patient with succinic semialdehyde dehydrogenase deficiency

Journal of Chromatography B: Analytical Technologies in the Biomedical and Life Sciences

Volumn 792, Issue 1, 2003, Pages 99-106

  Shinka, Toshihiro ^a   Ohfu, Masafumi ^b   Hirose, Shinichi ^b   Kuhara, Tomiko ^a  

^a KANAZAWA MEDICAL UNIVERSITY   (Japan)

^b FUKUOKA UNIVERSITY SCHOOL OF MEDICINE   (Japan)

Author keywords

Succinic semialdehyde dehydrogenase deficiency; Valproic acid

Indexed keywords

ENZYMES; GAS CHROMATOGRAPHY; ISOTOPES; MASS SPECTROMETERS;

ISOTOPE DILUTION TECHNIQUE;

BIOMEDICAL ENGINEERING;

3 DEOXYTETRONATE; 3,4 DIHYDROXYBUTYRIC ACID; 4 HYDROXYBUTYRIC ACID; 4 HYDROXYVALPROATE; 4,5 DIHYDROHEXANOATE; 5 HYDROXYVALPROATE; HEXANOIC ACID DERIVATIVE; SUCCINATE SEMIALDEHYDE DEHYDROGENASE; TETRONIC ACID DERIVATIVE; UNCLASSIFIED DRUG; VALPROIC ACID; VALPROIC ACID DERIVATIVE;

4 AMINOBUTYRIC ACID METABOLISM; AGE; CASE REPORT; CONFERENCE PAPER; CONTROLLED STUDY; DRUG EFFECT; DRUG EXCRETION; DRUG MECHANISM; EPILEPSY; GAS CHROMATOGRAPHY; HUMAN; INBORN ERROR OF METABOLISM; INFANT; ISOTOPE DILUTION ASSAY; MALE; MASS SPECTROMETRY; PRIORITY JOURNAL; QUANTITATIVE ANALYSIS; SUCCINIC SEMIALDEHYDE DEHYDROGENASE DEFICIENCY; URINALYSIS; URINARY EXCRETION; URINE LEVEL;

EID: 0038121890     PISSN: 15700232     EISSN: None     Source Type: Journal    
DOI: 10.1016/S1570-0232(03)00276-9     Document Type: Conference Paper

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