The Wlds mutation delays robust loss of motor and sensory axons in a genetic model for myelin-related axonopathy

Journal of Neuroscience

Volumn 23, Issue 7, 2003, Pages 2833-2839

  Samsam, Mohtashem ^a   Mi, Weiqian ^b   Wessig, Carsten ^a   Zielasek, Jürgen ^a   Toyka, Klaus V ^a   Coleman, Michael P ^b   Martini, Rudolf ^a  

^a UNIVERSITY OF WÜRZBURG   (Germany)

^b UNIVERSITY OF COLOGNE   (Germany)

Author keywords

Inherited neuropathies; Myelin mutant; Peripheral nervous system; Protein zero; Schwann cell; Wallerian degeneration

Indexed keywords

AGE; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL GENETICS; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; BREEDING; CELL SURVIVAL; DEMYELINATING DISEASE; GENE; GENE EXPRESSION; GENE FUSION; GENE MUTATION; MOTONEURON; MOUSE; MUSCLE ACTION POTENTIAL; MUSCLE STRENGTH; NERVE DEGENERATION; NEUROPATHY; NMNAT GENE; NONHUMAN; NUCLEOTIDE SEQUENCE; NULL ALLELE; PERIPHERAL NERVOUS SYSTEM; PRIORITY JOURNAL; SCHWANN CELL; SENSORY NERVE CELL; SPONTANEOUS MUTATION; UBE4B GENE; WLDS GENE; ACTION POTENTIAL; ANIMAL; BIOLOGICAL MODEL; C57BL MOUSE; ELECTRIC CONDUCTIVITY; GENETICS; INNERVATION; KINETICS; METABOLISM; MOUSE MUTANT; MUTATION; NERVE FIBER; PATHOLOGY; PERIPHERAL NERVE; PHYSIOLOGY; SKELETAL MUSCLE;

MYELIN PROTEIN; NERVE PROTEIN; WLD PROTEIN, MOUSE;

ACTION POTENTIALS; AGE FACTORS; ANIMALS; AXONS; DEMYELINATING DISEASES; ELECTRIC CONDUCTIVITY; KINETICS; MICE; MICE, INBRED C57BL; MICE, NEUROLOGIC MUTANTS; MODELS, GENETIC; MOTOR NEURONS; MUSCLE, SKELETAL; MUTATION; MYELIN P0 PROTEIN; NERVE TISSUE PROTEINS; NEURONS, AFFERENT; PERIPHERAL NERVES; WALLERIAN DEGENERATION;

EID: 0037388411     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.23-07-02833.2003     Document Type: Article

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