Mitochondrial dysfunction in myofibrillar myopathy

Neuropathology and Applied Neurobiology

Volumn 29, Issue 1, 2003, Pages 45-51

  Reimann, Jens ^a,b   Kunz, Wolfram S ^a   Vielhaber, Stefan ^c   Kappes Horn, Karin ^a   Schröder, Rolf ^a  

^a UNIVERSITY OF BONN   (Germany)

^b HAMMERSMITH HOSPITAL   (United Kingdom)

^c OTTO VON GUERICKE UNIVERSITY   (Germany)

Author keywords

Cytochrome c oxidase; Intermediate filaments; Mitochondria; Mitochondrial diseases; Muscle; Muscular diseases; Respiratory chain

Indexed keywords

CYTOCHROME C OXIDASE; CYTOTOXIC AGENT; DESMIN; MITOCHONDRIAL ENZYME; NICOTINAMIDE ADENINE DINUCLEOTIDE; OXIDOREDUCTASE; PLECTIN; REDUCED NICOTINAMIDE ADENINE DINUCLEOTIDE DEHYDROGENASE (UBIQUINONE); SUCCINATE DEHYDROGENASE;

ADULT; AGED; ANIMAL MODEL; ARTICLE; CLINICAL ARTICLE; ENCEPHALOMYOPATHY; FEMALE; GENE DELETION; GENE MUTATION; GENETIC SCREENING; HISTOCHEMISTRY; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; INTERMEDIATE FILAMENT; LACTIC ACIDOSIS; MALE; MITOCHONDRIAL MYOPATHY; MUSCLE ATROPHY; MUSCLE MITOCHONDRION; MYOCLONUS EPILEPSY; MYOPATHY; NONHUMAN; POINT MUTATION; PRIORITY JOURNAL; RESPIRATORY CHAIN; SKELETAL MUSCLE; STROKE;

AGED; DESMIN; FEMALE; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; MICROSCOPY, ELECTRON; MIDDLE AGED; MITOCHONDRIA; MITOCHONDRIAL MYOPATHIES; MULTIENZYME COMPLEXES; MUSCLE, SKELETAL; MYOFIBRILS;

EID: 0037327525     PISSN: 03051846     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2990.2003.00428.x     Document Type: Article

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