Plasma therapy in von Willebrand factor protease deficiency

Pediatric Nephrology

Volumn 17, Issue 10, 2002, Pages 867-870

  Deschênes, Georges ^a,d   Veyradier, Agnès ^b   Cloarec, Sylvie ^a   Benoit, Stéphane ^a   Desbois, Isabelle ^c   Gruel, Yves ^d   Nivet, Hubert ^a  

^a Centre de Pediatrie Clocheville   (France)

^b HÔPITAL ANTOINE BÉCLÈRE   (France)

^c CHU BRETONNEAU   (France)

^d SERVICE DE DERMATOLOGIE   (France)

Author keywords

Fresh frozen plasma; Hemolytic uremic syndrome; Recurrence of hemolytic uremic syndrome; Renal transplant; Thrombotic thrombocytopathic purpura; Von Willebrand factor cleaving protease

Indexed keywords

AZATHIOPRINE; CYCLOSPORIN; FRESH FROZEN PLASMA; IMMUNOSUPPRESSIVE AGENT; METHYLPREDNISOLONE; PREDNISONE; PROTEINASE; THYMOCYTE ANTIBODY; VON WILLEBRAND FACTOR;

ARTICLE; BRAIN ISCHEMIA; CASE REPORT; CEREBROVASCULAR ACCIDENT; CHILD; ENZYME DEFICIENCY; EXCHANGE BLOOD TRANSFUSION; GRAFT FAILURE; GRAFT VERSUS HOST REACTION; HEMODIALYSIS; HEMOLYTIC ANEMIA; HEMOLYTIC UREMIC SYNDROME; HUMAN; JAUNDICE; KIDNEY FAILURE; KIDNEY TRANSPLANTATION; LONG TERM CARE; MALE; NEPHRECTOMY; NEWBORN PERIOD; PLASMA TRANSFUSION; PRIORITY JOURNAL; RECURRENT DISEASE; RETINA ISCHEMIA; VON WILLEBRAND DISEASE;

ADOLESCENT; CEREBROVASCULAR DISORDERS; GRAFT REJECTION; HEMOLYTIC-UREMIC SYNDROME; HUMANS; KIDNEY FAILURE, CHRONIC; KIDNEY TRANSPLANTATION; MALE; NEPHRECTOMY; PLASMA; PLASMA EXCHANGE; PLATELET COUNT; RECURRENCE; VON WILLEBRAND FACTOR;

EID: 0036956049     PISSN: 0931041X     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00467-002-0944-9     Document Type: Article

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