Localization of biotinidase in the brain: Implications for its role in hearing loss in biotinidase deficiency

Hearing Research

Volumn 173, Issue 1-2, 2002, Pages 62-68

  Heller, Andrew J ^a   Stanley, Christine ^a   Shaia, Wayne T ^a   Sismanis, Aristides ^a   Spencer, Robert F ^a   Wolf, Barry ^b,c  

^a VIRGINIA COMMONWEALTH UNIVERSITY SCHOOL OF MEDICINE   (United States)

^b Farmington   (United States)

^c UNIVERSITY OF CONNECTICUT   (United States)

Author keywords

Auditory; Biotinidase; Biotinidase deficiency; Deafness; Hearing; Hearing loss; Immunohistochemistry; Sensorineural

Indexed keywords

BIOTINIDASE; COMPLEMENTARY DNA;

ANIMAL TISSUE; ARTICLE; BRAIN; BRAIN LEVEL; BRAIN STEM; COCHLEAR NUCLEUS; CONTROLLED STUDY; ENZYME DEFICIENCY; HAIR CELL; HEARING; HEARING LOSS; HUMAN; HYBRIDIZATION; IMMUNOHISTOCHEMISTRY; IN VITRO STUDY; MALE; MOUSE; NONHUMAN; NORTHERN BLOTTING; PRIORITY JOURNAL; PROTEIN DETERMINATION; PROTEIN EXPRESSION; PROTEIN FUNCTION; PROTEIN LOCALIZATION; RAT; SPIRAL GANGLION; SUPERIOR OLIVARY NUCLEUS; TISSUE DISTRIBUTION;

AMIDOHYDROLASES; ANIMALS; BIOTINIDASE; BLOTTING, NORTHERN; BRAIN; DNA, COMPLEMENTARY; HEARING LOSS; HUMANS; IMMUNOHISTOCHEMISTRY; MALE; METABOLISM, INBORN ERRORS; MICE; POLYMERASE CHAIN REACTION; RATS; STAINING AND LABELING; TISSUE DISTRIBUTION;

EID: 0036837097     PISSN: 03785955     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0378-5955(02)00609-3     Document Type: Article

References (13)

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