-
1
-
-
0026621049
-
Primary structure of dystrophin-related protein
-
Tinsley J.M., Blake D.J., Roche A., et al. Primary structure of dystrophin-related protein. Nature. 360:1992;591-592.
-
(1992)
Nature
, vol.360
, pp. 591-592
-
-
Tinsley, J.M.1
Blake, D.J.2
Roche, A.3
-
2
-
-
0024987672
-
Présence d'une protéine de type dystrophine au niveau de la jonction neuromusculaire dans la dystrophie musculaire de Duchenne et la souris mutante 'mdx'
-
Fardeau M., Tomé F.M.S., Collin H., et al. Présence d'une protéine de type dystrophine au niveau de la jonction neuromusculaire dans la dystrophie musculaire de Duchenne et la souris mutante 'mdx'. C R Acad Sci Paris. 311:1990;197-204.
-
(1990)
C R Acad Sci Paris
, vol.311
, pp. 197-204
-
-
Fardeau, M.1
Tomé, F.M.S.2
Collin, H.3
-
3
-
-
0025932274
-
Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle
-
Khurana T.S., Watkins S.C., Chafey P., et al. Immunolocalization and developmental expression of dystrophin related protein in skeletal muscle. Neuromuscul Disord. 1:1991;185-194.
-
(1991)
Neuromuscul Disord
, vol.1
, pp. 185-194
-
-
Khurana, T.S.1
Watkins, S.C.2
Chafey, P.3
-
4
-
-
0027358450
-
Reciprocal expression of dystrophin and utrophin in muscles of Duchenne muscular dystrophy patients, female DMD carriers and control subjects
-
Mizumo Y., Nonaka I., Hirai S., et al. Reciprocal expression of dystrophin and utrophin in muscles of Duchenne muscular dystrophy patients, female DMD carriers and control subjects. J Neurol Sci. 119:1993;43-52.
-
(1993)
J Neurol Sci
, vol.119
, pp. 43-52
-
-
Mizumo, Y.1
Nonaka, I.2
Hirai, S.3
-
5
-
-
0029906168
-
Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene
-
Tinsley J.M., Potter A.C., Phelps S.R., Fisher R., Trickett J.I., Davies K.E. Amelioration of the dystrophic phenotype of mdx mice using a truncated utrophin transgene. Nature. 384:1996;349-353.
-
(1996)
Nature
, vol.384
, pp. 349-353
-
-
Tinsley, J.M.1
Potter, A.C.2
Phelps, S.R.3
Fisher, R.4
Trickett, J.I.5
Davies, K.E.6
-
6
-
-
0028047235
-
Dystrophin-glycoprotein complex: Its role in the molecular pathogenesis of muscular dystrophies
-
Matsumura K., Campbell K.P. Dystrophin-glycoprotein complex: its role in the molecular pathogenesis of muscular dystrophies. Muscle Nerve. 17:1994;2-15.
-
(1994)
Muscle Nerve
, vol.17
, pp. 2-15
-
-
Matsumura, K.1
Campbell, K.P.2
-
7
-
-
0028837008
-
Calcium/calmodulin-dependent regulation of the NH2 terminal F-actin binding domain of utrophin
-
Winder S.J., Kendrick-Jones J. Calcium/calmodulin-dependent regulation of the NH2 terminal F-actin binding domain of utrophin. FEBS Lett. 357:1995;125-128.
-
(1995)
FEBS Lett
, vol.357
, pp. 125-128
-
-
Winder, S.J.1
Kendrick-Jones, J.2
-
8
-
-
0033382340
-
Understanding dystrophinopathies: An inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse [In Process Citation]
-
Gillis J.M. Understanding dystrophinopathies: an inventory of the structural and functional consequences of the absence of dystrophin in muscles of the mdx mouse [In Process Citation]. J Muscle Res Cell Motil. 20:1999;605-625.
-
(1999)
J Muscle Res Cell Motil
, vol.20
, pp. 605-625
-
-
Gillis, J.M.1
-
9
-
-
0025301397
-
A noninvasive procedure to detect muscle weakness in the mdx mouse
-
Carlson C.G., Makiejus R.V. A noninvasive procedure to detect muscle weakness in the mdx mouse. Muscle Nerve. 13:1990;480-484.
-
(1990)
Muscle Nerve
, vol.13
, pp. 480-484
-
-
Carlson, C.G.1
Makiejus, R.V.2
-
10
-
-
0025662048
-
Dystrophin-deficient mdx muscle fibers are preferentially vulnerable to necrosis induced by experimental lengthening contractions
-
Weller B., Karpati G., Carpenter S. Dystrophin-deficient mdx muscle fibers are preferentially vulnerable to necrosis induced by experimental lengthening contractions. J Neurol Sci. 100:1990;9-13.
-
(1990)
J Neurol Sci
, vol.100
, pp. 9-13
-
-
Weller, B.1
Karpati, G.2
Carpenter, S.3
-
11
-
-
0027248618
-
Increased susceptibility of EDL muscles from mdx mice to damage induced by contractions with stretch
-
Moens P., Baatsen P.H.W.W., Maréchal G. Increased susceptibility of EDL muscles from mdx mice to damage induced by contractions with stretch. J Muscle Res Cell Motil. 14:1993;446-451.
-
(1993)
J Muscle Res Cell Motil
, vol.14
, pp. 446-451
-
-
Moens, P.1
Baatsen, P.H.W.W.2
Maréchal, G.3
-
12
-
-
0029918603
-
Functional protection of dystrophic mouse (mdx) muscles after adenovirus-mediated transfer of a dystrophin minigene
-
Deconinck N., Ragot T., Maréchal G., et al. Functional protection of dystrophic mouse (mdx) muscles after adenovirus-mediated transfer of a dystrophin minigene. Proc Natl Acad Sci USA. 93:1996;3570-3574.
-
(1996)
Proc Natl Acad Sci USA
, vol.93
, pp. 3570-3574
-
-
Deconinck, N.1
Ragot, T.2
Maréchal, G.3
-
13
-
-
0017797971
-
Intracellular calcium accumulation in Duchenne dystrophy and other myopathies: A study of 567,000 muscle fibres in 114 biopsies
-
Bodensteiner J.B., Engel A.G. Intracellular calcium accumulation in Duchenne dystrophy and other myopathies: a study of 567,000 muscle fibres in 114 biopsies. Neurology. 28:1978;439-446.
-
(1978)
Neurology
, vol.28
, pp. 439-446
-
-
Bodensteiner, J.B.1
Engel, A.G.2
-
14
-
-
0027234619
-
Critical evaluation of cytosolic calcium determination in resting muscle fibres from normal and dystrophic (mdx) mice
-
Gailly P., Boland B., Himpens B., et al. Critical evaluation of cytosolic calcium determination in resting muscle fibres from normal and dystrophic (mdx) mice. Cell Calcium. 14:1993;473-483.
-
(1993)
Cell Calcium
, vol.14
, pp. 473-483
-
-
Gailly, P.1
Boland, B.2
Himpens, B.3
-
15
-
-
0026347187
-
Increased calcium influx in dystrophic muscle
-
Turner P.R., Fong P., Denetclaw W.F., et al. Increased calcium influx in dystrophic muscle. J Cell Biol. 115:1991;1701-1712.
-
(1991)
J Cell Biol
, vol.115
, pp. 1701-1712
-
-
Turner, P.R.1
Fong, P.2
Denetclaw, W.F.3
-
16
-
-
0023739851
-
Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice
-
Turner P.R., Westwood T., Regen C.M., et al. Increased protein degradation results from elevated free calcium levels found in muscle from mdx mice. Nature. 355:1988;735-738.
-
(1988)
Nature
, vol.355
, pp. 735-738
-
-
Turner, P.R.1
Westwood, T.2
Regen, C.M.3
-
17
-
-
0028414945
-
2+ concentrations are not elevated in resting cultured muscle from Duchenne (DMD) patients and in MDX mouse muscle fibres
-
2+ concentrations are not elevated in resting cultured muscle from Duchenne (DMD) patients and in MDX mouse muscle fibres. Pflügers Arch. 426:1994;499-505.
-
(1994)
Pflügers Arch
, vol.426
, pp. 499-505
-
-
Pressmar, J.1
Brinkmeier, H.2
Seewald, M.J.3
-
18
-
-
0033569656
-
Intracellular calcium signals measured with indo-1 in isolated skeletal muscle fibres from control and mdx mice
-
Collet C., Allard B., Tourneur Y., et al. Intracellular calcium signals measured with indo-1 in isolated skeletal muscle fibres from control and mdx mice. J Physiol. 520:1999;417-429.
-
(1999)
J Physiol
, vol.520
, pp. 417-429
-
-
Collet, C.1
Allard, B.2
Tourneur, Y.3
-
19
-
-
0033559330
-
Increased calcium entry into dystrophin-deficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers
-
Tutdibi O., Brinkmeier H., Rudel R., et al. Increased calcium entry into dystrophin-deficient muscle fibres of MDX and ADR-MDX mice is reduced by ion channel blockers. J Physiol. 515:1999;859-868.
-
(1999)
J Physiol
, vol.515
, pp. 859-868
-
-
Tutdibi, O.1
Brinkmeier, H.2
Rudel, R.3
-
20
-
-
0030273325
-
Hypoosmotic shocks induce elevation of resting calcium level in Duchenne muscular dystrophy myotubes contracting in vitro
-
Imbert N., Vandebrouck C., Constantin B., et al. Hypoosmotic shocks induce elevation of resting calcium level in Duchenne muscular dystrophy myotubes contracting in vitro. Neuromuscul Disord. 6:1996;351-360.
-
(1996)
Neuromuscul Disord
, vol.6
, pp. 351-360
-
-
Imbert, N.1
Vandebrouck, C.2
Constantin, B.3
-
22
-
-
0030723508
-
Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice
-
Deconinck N., Tinsley J., De Backer F., et al. Expression of truncated utrophin leads to major functional improvements in dystrophin-deficient muscles of mice. Nat Med. 3:1997;1216-1221.
-
(1997)
Nat Med
, vol.3
, pp. 1216-1221
-
-
Deconinck, N.1
Tinsley, J.2
De Backer, F.3
-
23
-
-
0031727771
-
Expression of full-length utrophin prevents muscular dystrophy in mdx mice
-
Tinsley J., Deconinck N., Fisher R., et al. Expression of full-length utrophin prevents muscular dystrophy in mdx mice. Nat Med. 4:1998;1441-1444.
-
(1998)
Nat Med
, vol.4
, pp. 1441-1444
-
-
Tinsley, J.1
Deconinck, N.2
Fisher, R.3
-
24
-
-
0034641893
-
Mdx mice inducibly expressing dystrophin provide insights into the potential of gene therapy for Duchenne muscular dystrophy
-
Ahmad A., Brinson M., Hodges B.L., et al. Mdx mice inducibly expressing dystrophin provide insights into the potential of gene therapy for Duchenne muscular dystrophy. Hum Mol Genet. 9:2000;2507-2515.
-
(2000)
Hum Mol Genet
, vol.9
, pp. 2507-2515
-
-
Ahmad, A.1
Brinson, M.2
Hodges, B.L.3
-
25
-
-
0030848969
-
Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy
-
Deconinck A.E., Rafael J.A., Skinner J.A., et al. Utrophin-dystrophin-deficient mice as a model for Duchenne muscular dystrophy. Cell. 90:1997;717-727.
-
(1997)
Cell
, vol.90
, pp. 717-727
-
-
Deconinck, A.E.1
Rafael, J.A.2
Skinner, J.A.3
|