α1 antitrypsin deficiency in a patient with systemic vasculitis and primary Sjögren's syndrome

Annals of the Rheumatic Diseases

Volumn 61, Issue 10, 2002, Pages 945-946

  Lindström, Folke D ^a   Skogh, T ^a   Lundstrom I M C ^a  

^a LINKÖPING UNIVERSITY HOSPITAL   (Sweden)

Author keywords

[No Author keywords available]

Indexed keywords

ACUTE PHASE PROTEIN; ALPHA 1 ANTITRYPSIN; CYCLOPHOSPHAMIDE; METHYLPREDNISOLONE;

ADULT; ALPHA 1 ANTITRYPSIN DEFICIENCY; ARTHRITIS; AUTOIMMUNE DISEASE; CASE REPORT; CLINICAL FEATURE; FEMALE; HUMAN; LETTER; PHENOTYPE; PRIORITY JOURNAL; PROGNOSIS; SJOEGREN SYNDROME; SYSTEMIC VASCULITIS;

ADULT; ALPHA 1-ANTITRYPSIN DEFICIENCY; FEMALE; HUMANS; SJOGREN'S SYNDROME; VASCULITIS;

EID: 0036786343     PISSN: 00034967     EISSN: None     Source Type: Journal    
DOI: 10.1136/ard.61.10.945     Document Type: Letter

References (12)

1. Potempa J, Korzus E, Travis J. The serpin superfamily of proteinase inhibitors: structure, function and regulation. J Biol Chem 1994;269:15957-60.
2. Eriksson S. Pulmonary emphysema and alfa-1-antitrypsin deficiency. Acta Med Scand 1964;175:197-205.
3. Carrell RW, Lomas DA. Alpha-1 antitrypsin deficiency - a model for conformational disease. N Engl J Med 2002;346:45-53.
4. Elzouki A-N, Segelmark M, Wieslander J, Eriksson S. Strong link between the alpha-1-antitrypsin PiZ allele and Wegener's granulomatosis. J Intern Med 1994;236:543-8.
5. Segelmark M, Elzouki A-N, Wieslander J, Eriksson S. The PiZ gene of alpha-1-antitrypsin as a determinant of outcome in PR3-ANCA positive vasculitis. Kidney Int 1995;48:844-50.
6. Fearnley IR, Spalton DJ, Milford Ward A, Slavin B, Muncey F. I Alpha-1-antitrypsin phenotypes in acute anterior uveitis. Br J Ophthalmol 1988;72:636-9.
7. Karsh J, Vergalla J, Anthony Jones E. Alpha-1-antitrypsin phenotypes in rheumatoid arthritis and systemic lupus erythematosus. Arthritis Rheum 1979;22:111-13.
8. Vitali C, Bombardieri S, Moutsopoulos HM, Coll J, Gerli R, Hatron PY, et al. Assessment of the European classification criteria for Sjögren's syndrome in a series of clinically defined cases: results of a prospective multicentre study. Ann Rheum Dis 1996;55:116-21.
9. Manthorpe R, Oxholm P, Prause JU, Schiodt M. The Copenhagen criteria for Sjögren's syndrome. Scand J Rheumatol 1986;15(suppl 61):19-21.
10. Wallmark A, Alm R, Eriksson S. Monoclonal antibody specific for the mutant PiZ alfa-1-antitrypsin and its application in an ELISA procedure for identification of PiZ gene carriers. Proc Natl Acad Sci USA 1984;81:5690-3.
11. Jeppson JO, Frantzén B. Typing of genetic variants of alfa-1-antitrypsin by electrofocusing. Clin Chem 1982;28:219-22.
12. Hersey P, Lawrence S, Prendergast D, Bindon C, Benson W, Valk P. Association of Sjögren's syndrome with C4 deficiency, defective reticuloendothelial function and circulating immune complexes. Clin Exp Immunol 1983;52:551-60.