Bones benefit from better biochemical control in type 1 glycogen storage disease

Journal of Pediatrics

Volumn 141, Issue 3, 2002, Pages 308-310

  Wolfsdorf, Joseph I ^a  

^a BOSTON CHILDREN S HOSPITAL   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

GLUCOSE 6 PHOSPHATE DEHYDROGENASE;

BONE MASS; CATALYSIS; EDITORIAL; GLUCONEOGENESIS; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HYPOGLYCEMIA; METABOLIC REGULATION; PRIORITY JOURNAL; RISK BENEFIT ANALYSIS;

EID: 0036732562     PISSN: 00223476     EISSN: None     Source Type: Journal    
DOI: 10.1067/mpd.2002.127504     Document Type: Article

References (20)

1. Glucose-6-phosphatase of the liver in glycogen storage disease
2. Roentgenographic skeletal changes in the glycogen storage diseases
3. Radiography of glycogen storage diseases
4. Pathologic studies of the osteoporosis of Von Gierke's disease (glycogenosis 1a)
5. Portal diversion for the treatment of glycogen storage disease in humans
6. Glycogen storage diseases. Phenotypic, genetic, and biochemical characteristics, and therapy
7. Portacaval shunt for glycogen storage disease: Value of prolonged intravenous hyperalimentation before surgery
8. Type I glycogen storage disease: Five years of management with nocturnal intragastric feeding
9. The long-term outcome of patients with glycogen storage disease type Ia
10. Effect of continuous glucose therapy begun in infancy on the long-term clinical course of patients with type I glycogen storage disease
11. Type 1 glycogen storage disease: A metabolic basis for advances in treatment
12. Physical growth and development of children with type 1 glycogen-storage disease: Comparison of the effects of long-term use of dextrose and uncooked cornstarch
13. Glycogen storage disease: Effects of glucose infusions on [15N] glycine kinetics and nitrogen metabolism
14. Effect of continuous glucose therapy with uncooked cornstarch on the long-term clinical course of type 1a glycogen storage disease
15. Acquisition of optimal bone mass in childhood and adolescence
16. Current concepts in pediatric bone disease
17. Muscle strength, bone mass, and age-related bone loss
18. Neutropenia, neutrophil dysfunction, and inflammatory bowel disease in glycogen storage disease type Ib: Results of the European Study on Glycogen Storage Disease type I
19. Low bone mass in glycogen storage disease type 1 is associated with reduced muscle force and poor metabolic control
20. Bone, acid, and osteoporosis