Long-term perspectives for 46,XY patients affected by complete androgen insensitivity syndrome or congenital micropenis

Seminars in Reproductive Medicine

Volumn 20, Issue 3, 2002, Pages 297-304

  Wisniewski, Amy B ^a   Migeon, Claude J ^a  

^a JOHNS HOPKINS UNIVERSITY SCHOOL OF MEDICINE   (United States)

Author keywords

Androgen insensitivity; Gender; Intersex; Micropenis; Sex

Indexed keywords

ADULT; AGED; ANDROGEN INSENSITIVITY SYNDROME; CLINICAL ARTICLE; FEMALE; FEMININITY; FOLLOW UP; HUMAN; KARYOTYPE 46,XY; LONG TERM CARE; MALE; MICROPENIS; OUTCOMES RESEARCH; PATIENT EDUCATION; PATIENT SATISFACTION; PLASTIC SURGERY; REARING; REVIEW; SEX DIFFERENTIATION DISORDER; SEXUAL FUNCTION; TREATMENT PLANNING;

ABNORMALITIES; ADULT; ANDROGEN-INSENSITIVITY SYNDROME; FEMALE; GENDER IDENTITY; GONADAL DYSGENESIS, 46,XY; HUMANS; LONGITUDINAL STUDIES; MALE; MIDDLE AGED; PATIENT SATISFACTION; PENIS; SEXUAL BEHAVIOR; TREATMENT OUTCOME;

EID: 0036669348     PISSN: 15268004     EISSN: None     Source Type: Journal    
DOI: 10.1055/s-2002-35376     Document Type: Review

References (20)

1. Birnbacher R, Marberger M, Weissenbacher G, Schober E, Frisch H. Gender identity reversal in an adolescent with mixed gonadal dysgenesis. J Pediatr Endocrinol Metab 1999;12:687-690
2. Phornphutkul C, Fausto-Sterling A, Gruppuso PA. Gender self-reassignment in an XY adolescent female born with ambiguous genitalia. Pediatrics 2000;106:135-137
3. Reiner WG. Case study: Sex reassignment in a teenage girl. J Am Acad Child Adolesc Psychiatry 1996;35:799-803
4. Daaboul J, Frader J. Ethics and the management of the patient with intersex: A middle way. J Pediatr Endocrinol Metab 2001;14:1575-1583
5. Wisniewski AB, Migeon CJ, Meyer-Bahlburg HFL, et al. Complete androgen insensitivity syndrome: Long-term medical, surgical and psychosexual outcome. J Clin Endocrinol Metab 2000;85:2664-2669
6. Wisniewski AB, Migeon CJ, Gearhart JP, et al. Congenital micropenis: Long-term medical, surgical and psychosexual follow-up of individuals raised male or female. Horm Res 2001;56:3-11
7. Lewis VG, Money J. Gender-identity/role: G-I/R Part A: XY (androgen-insensitive) syndrome and XX (Rokitansky) syndrome of vaginal atresia. In: Dennerstein L, Burrows GD, eds. Handbook of Psychosomatic Obstetrics and Gynaecology. New York: Elsevier Biomedical Press; 1983:51-60
8. Masica DN, Money J, Ehrhardt AA. Fetal feminization and female gender identity in the testicular feminizing syndrome of androgen insensitivity. Arch Sex Behav 1971;1:131-142
9. Migeon CJ, Brown TR, Fichman KR. Androgen insensitivity syndrome. In: Josso N, ed. The Intersex Child: Pediatric and Adolescent Endocrinology. Basel, Switzerland: Karger; 1981:171-202
10. Money J, Ehrhardt AA, Masica DN. Fetal feminization induced by androgen insensitivity in the testicular feminizing syndrome: Effect on marriage and maternalism. Johns Hopkins Med J 1968;123:105-114
11. Money J, Schwartz M, Lewis VG. Adult erotosexual status and fetal hormonal masculinization and demasculinization: 46,XX congenital virilizing adrenal hyperplasia and 46,XY androgen-insensitivity syndrome compared. Psychoneuroendocrinology 1984;9:405-414
12. Quigley CA, De Bellis A, Marschke KB, et al. Androgen receptor defects: Historical, clinical and molecular perspectives. Endocr Rev 1995;16:271-321
13. Migeon CJM, Berkovitz G, Brown TR. Sexual differentiation and ambiguity. In: Kappy MS, Blizzard RM, Migeon CJ, eds. Wilkins, The Diagnosis and Treatment of Endocrine Disorders in Childhood and Adolescence. 4th Ed. Springfield, IL: Charles C Thomas; 1994:573-715
14. Polani PE. Hormonal and clinical aspects of hermaphroditism and the testicular feminizing syndrome in man. Philos Trans R Soc Lond B Biol Sci 1970;259:187-204
15. Kinsey AC, Pomeroy WB, Martin CE. Sexual Behavior in the Human Male. Philadelphia: WB Saunders; 1948:638
16. Aaronson IA. Micropenis: Medical and surgical implications. J Urol 1994;152:4-14
17. Lee PA, Mazur T, Danish R, et al. Micropenis: I. Criteria, etiologies and classification. Johns Hopkins Med J 1980;146:156-163
18. Bin-Abbas B, Conte F, Grumbach MM, Kaplan S. Congenital hypogonadotropic hypogonadism and micropenis: Effect of testosterone treatment on adult penile size - Why sex reversal is not indicated. J Pediatr 1999;134:579-583
19. Money J, Lehne GK, Pierre-Jerome F. Micropenis: Adult follow-up and comparison of size against new norms. J Sex Marital Ther 1984;10:105-116
20. Reilly JM, Woodhouse CRJ. Small penis and the male sexual role. J Urol 1989;142:569-571