Vascular Defects and Sensorineural Deafness in a Mouse Model of Norrie Disease

Journal of Neuroscience

Volumn 22, Issue 11, 2002, Pages 4286-4292

  Rehm, Heidi L ^a,b,c   Zhang, Duan Sun ^a,c   Brown, M Christian ^b,d   Burgess, Barbara ^d   Halpin, Chris ^b,d   Berger, Wolfgang ^e   Morton, Cynthia C ^b,f   Corey, David P ^a,b,c   Chen, Zheng Yi ^a,b  

^a MASSACHUSETTS GENERAL HOSPITAL   (United States)

^b HARVARD MEDICAL SCHOOL   (United States)

^c HOWARD HUGHES MEDICAL INSTITUTE   (United States)

^d MASSACHUSETTS EYE AND EAR INFIRMARY   (United States)

^e MAX PLANCK INSTITUTE FOR MOLECULAR GENETICS   (Germany)

^f BRIGHAM AND WOMEN S HOSPITAL   (United States)

Author keywords

Angiogenesis; Blindness; Cochlea; Deafness; Marginal cells; Mouse model; Norrie disease; Norrin; Retina; Stria vascularis; Vascular

Indexed keywords

FLUORESCENT DYE; EYE PROTEIN; NDP PROTEIN, HUMAN; NDPH PROTEIN, MOUSE; NERVE PROTEIN;

ADULT; ANIMAL CELL; ANIMAL EXPERIMENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; AUDIOLOGY; COCHLEA; CONTROLLED STUDY; DISEASE MODEL; EXPERIMENTAL MOUSE; GENE DISRUPTION; HEARING; HEARING LOSS; HISTOLOGY; HUMAN; KNOCKOUT MOUSE; MOUSE; NONHUMAN; NORRIE DISEASE; PERCEPTION DEAFNESS; PHENOTYPE; PRIORITY JOURNAL; STRIA VASCULARIS; VASCULAR DISEASE; VASCULARIZATION; ANIMAL; AUDITORY STIMULATION; AUDITORY THRESHOLD; BLINDNESS; BLOOD VESSEL; DISEASE COURSE; EVOKED BRAIN STEM AUDITORY RESPONSE; GENETICS; MENTAL DEFICIENCY; MOUSE MUTANT; PATHOLOGY; PATHOPHYSIOLOGY; PURE TONE AUDIOMETRY; RECESSIVE GENE; RETINA; SYNDROME; VESTIBULAR TEST; X CHROMOSOME;

ACOUSTIC STIMULATION; ADULT; ANIMALS; AUDIOMETRY, PURE-TONE; AUDITORY THRESHOLD; BLINDNESS; BLOOD VESSELS; COCHLEA; DISEASE MODELS, ANIMAL; DISEASE PROGRESSION; EVOKED POTENTIALS, AUDITORY, BRAIN STEM; EYE PROTEINS; FLUORESCENT DYES; GENES, RECESSIVE; HEARING LOSS, SENSORINEURAL; HUMANS; MENTAL RETARDATION; MICE; MICE, KNOCKOUT; NERVE TISSUE PROTEINS; PHENOTYPE; RETINA; STRIA VASCULARIS; SYNDROME; VESTIBULAR FUNCTION TESTS; X CHROMOSOME;

EID: 0036615753     PISSN: 02706474     EISSN: None     Source Type: Journal    
DOI: 10.1523/jneurosci.22-11-04286.2002     Document Type: Article

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