Successful treatment of congenital thrombotic thrombocytopenic purpura using the intermediate purity factor VIII concentrate BPL 8Y

British Journal of Haematology

Volumn 119, Issue 1, 2002, Pages 176-179

  Lester, Will A ^a   Williams, Michael D ^a,c   Allford, Sarah L ^b   Enayat, M Said ^a   Machin, Samuel J ^b  

^a BIRMINGHAM CHILDREN S HOSPITAL   (United Kingdom)

^b UNIVERSITY COLLEGE LONDON   (United Kingdom)

^c BIRMINGHAM CHILDREN S HOSPITAL NHS FOUNDATION TRUST   (United Kingdom)

Author keywords

Congenital thrombotic thrombocytopenic purpura; Fresh frozen plasma; Intermediate purity factor VIII concentrate; Microangiopathy; Von Willebrand factor cleaving protease

Indexed keywords

BLOOD CLOTTING FACTOR 8 CONCENTRATE; FRESH FROZEN PLASMA; PROTEINASE; UNCLASSIFIED DRUG; VON WILLEBRAND FACTOR CLEAVING PROTEINASE;

ADOLESCENT; ARTICLE; ASSAY; CASE REPORT; FEMALE; HUMAN; PRIORITY JOURNAL; PROPHYLAXIS; QUANTITATIVE ANALYSIS; THROMBOTIC THROMBOCYTOPENIC PURPURA;

ADOLESCENT; ANTIGENS; FACTOR VIII; FEMALE; HUMANS; L-LACTATE DEHYDROGENASE; PLATELET COUNT; PURPURA, THROMBOTIC THROMBOCYTOPENIC; TREATMENT OUTCOME;

EID: 0036400230     PISSN: 00071048     EISSN: None     Source Type: Journal    
DOI: 10.1046/j.1365-2141.2002.03809.x     Document Type: Article

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