Familial isolated congenital asplenia: A rare, frequently hereditary dominant condition, often detected too late as a cause of overwhelming pneumococcal sepsis. Report of a new case and review of 31 others

European Journal of Pediatrics

Volumn 161, Issue 7, 2002, Pages 368-372

  Gilbert, Brigitte ^a   Menetrey, Céline ^b   Belin, Valérie ^b   Brosset, Philippe ^b   De Lumley, Lionel ^b   Fisher, Alain ^c  

^a DUPUYTREN UNIVERSITY HOSPITAL   (France)

^b LIMOGES UNIVERSITY HOSPITAL   (France)

^c HÔPITAL NECKER ENFANTS MALADES   (France)

Author keywords

Familial asplenia; Howell Jolly bodies; Isolated congenital asplenia; Pneumococcal sepsis

Indexed keywords

AMOXICILLIN; ANTIBIOTIC AGENT; CEFOTAXIME; PENICILLIN G; PNEUMOCOCCUS VACCINE; VANCOMYCIN;

ADULT; ANTIBIOTIC PROPHYLAXIS; ANTIBIOTIC SENSITIVITY; ARTICLE; ASPLENIA; BACTERIAL MENINGITIS; BLOOD SMEAR; CHILD; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DISEASE COURSE; FEMALE; HUMAN; INFANT; LABORATORY TEST; MALE; PRIORITY JOURNAL; SEPSIS; SEROTYPE; STREPTOCOCCUS PNEUMONIAE; TREATMENT OUTCOME; ULTRASOUND; VACCINATION;

ABNORMALITIES; ANTI-BACTERIAL AGENTS; BACTEREMIA; DRUG THERAPY, COMBINATION; ERYTHROCYTE INCLUSIONS; FATAL OUTCOME; FEMALE; HUMANS; INFANT; PNEUMONIA, PNEUMOCOCCAL; RISK ASSESSMENT; SEVERITY OF ILLNESS INDEX; SPLEEN; STREPTOCOCCUS PNEUMONIAE;

EID: 0036304562     PISSN: 03406199     EISSN: None     Source Type: Journal    
DOI: 10.1007/s00431-002-0965-1     Document Type: Article

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