Clinical and morphological features including expression of βig-h3 and keratan sulphate proteoglycans in Maroteaux-Lamy syndrome type B and in normal cornea

British Journal of Ophthalmology

Volumn 86, Issue 2, 2002, Pages 147-151

  Akhtar, Saeed ^a   Tullo, Andrew ^d   Caterson, Bruce ^b   Davies, Janet R ^b   Bennett, Kelly ^c   Meek, Keith M ^a  

^a CARDIFF UNIVERSITY   (United Kingdom)

^b CARDIFF UNIVERSITY   (United Kingdom)

^c BRISTOL MYERS SQUIBB   (United States)

^d MANCHESTER ROYAL EYE HOSPITAL   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BETA IG H3 PROTEIN; COLLAGEN FIBRIL; GENE PRODUCT; KERATAN SULFATE; N ACETYLGALACTOSAMINE 4 SULFATASE; PROTEOGLYCAN; UNCLASSIFIED DRUG;

ADOLESCENT; APOPTOSIS; ARTICLE; CASE REPORT; CELL LABELING; CELL ORGANELLE; CLINICAL FEATURE; CORNEA; CORNEA EPITHELIUM; ENDOTHELIUM CELL; FEMALE; FIBROGENESIS; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOELECTRON MICROSCOPY; KERATINOCYTE; LIGHT SCATTERING; MAROTEAUX LAMY SYNDROME; PATHOGENESIS; PRIORITY JOURNAL; PROTEIN EXPRESSION; STROMA CELL;

ADOLESCENT; CORNEA; EXTRACELLULAR MATRIX PROTEINS; FEMALE; HUMANS; KERATAN SULFATE; MICROSCOPY, ELECTRON; MUCOPOLYSACCHARIDOSIS VI; NEOPLASM PROTEINS; TRANSFORMING GROWTH FACTOR BETA;

EID: 0036163588     PISSN: 00071161     EISSN: None     Source Type: Journal    
DOI: 10.1136/bjo.86.2.147     Document Type: Article

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