Clinical, histopathologic, and ultrastructural characteristics of BIGH3(TGFBI) amyloid corneal dystrophies are supportive of the existence of a new type of LCD: The LCDi

Cornea

Volumn 21, Issue 5, 2002, Pages 463-468

  Schmitt Bernard, Clair Florent ^a,b   Schneider, Christelle ^a   Argilés, Àngel ^a  

^a MONTPELLIER UNIVERSITY HOSPITAL   (France)

^b INSTITUTE OF HUMAN GENETICS   (France)

Author keywords

Amyloidosis; BIGH3; Immunohistochemistry; Keratoepithelin; Lattice corneal dystrophies; TGFBI; Ultrastructural study

Indexed keywords

AMYLOID; ANTIBODY; CONGO RED; GENE PRODUCT; KERATOEPITHELIN; PROTEIN BIGH3; UNCLASSIFIED DRUG;

ADULT; AGED; AMYLOIDOSIS; ARTICLE; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; CORNEA; CORNEA DYSTROPHY; DISEASE CLASSIFICATION; FEMALE; HISTOPATHOLOGY; HUMAN; HUMAN TISSUE; IMMUNOHISTOCHEMISTRY; MALE; PRIORITY JOURNAL; SKIN BIOPSY; TRANSMISSION ELECTRON MICROSCOPY; ULTRASTRUCTURE;

AGED; AMYLOID; AMYLOIDOSIS; CONGO RED; CORNEA; CORNEAL DYSTROPHIES, HEREDITARY; EXTRACELLULAR MATRIX PROTEINS; FEMALE; HUMANS; IMMUNOENZYME TECHNIQUES; MALE; MIDDLE AGED; NEOPLASM PROTEINS; STAINING AND LABELING; TRANSFORMING GROWTH FACTOR BETA;

EID: 0036081322     PISSN: 02773740     EISSN: None     Source Type: Journal    
DOI: 10.1097/00003226-200207000-00006     Document Type: Article

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