Severe intrarenal fibrosis, infundibular stenosis, renal cysts, and persistent perilobar nephrogenic rests in a patient with Beckwith-Wiedemann syndrome 27 years after diffuse nephroblastomatosis and wilms tumor: Natural progression or a consequence of treatment?

Journal of Pediatric Hematology/Oncology

Volumn 24, Issue 5, 2002, Pages 389-393

  Kulkarni, Roshni ^a   Wolf Jr , J Stuart ^a   Padiyar, Niru ^a   Zuckerman, Leonard ^a   Gera, Renuka ^a   Scott Emuakpor, Ajovi B ^a  

^a MICHIGAN STATE UNIVERSITY   (United States)

Author keywords

Beckwith Wiedemann syndrome; Infundibular stenosis; Late effects; Nephroblastomatosis; Perilobar nephrogenic rests; Wilms tumor

Indexed keywords

DACTINOMYCIN; DOXORUBICIN; VINCRISTINE;

ADULT; ANALGESIA; ARTICLE; BALLOON DILATATION; BECKWITH WIEDEMANN SYNDROME; CASE REPORT; CAUTERIZATION; CLINICAL FEATURE; COMPUTER ASSISTED TOMOGRAPHY; DISEASE COURSE; FEMALE; GLOMERULOSCLEROSIS; HUMAN; HYSTEROSCOPE; KIDNEY BIOPSY; KIDNEY CALCIFICATION; KIDNEY CYST; KIDNEY FIBROSIS; KIDNEY SCAR; KIDNEY TRANSPLANTATION; NEPHRECTOMY; NEPHROBLASTOMA; PRIORITY JOURNAL; TREATMENT PLANNING;

ADULT; ANTINEOPLASTIC COMBINED CHEMOTHERAPY PROTOCOLS; BECKWITH-WIEDEMANN SYNDROME; BIOPSY, NEEDLE; DISEASE PROGRESSION; FEMALE; FIBROSIS; HUMANS; KIDNEY; KIDNEY CALCULI; KIDNEY DISEASES, CYSTIC; KIDNEY NEOPLASMS; KIDNEY TRANSPLANTATION; NEPHRECTOMY; RADIOTHERAPY; TOMOGRAPHY, X-RAY COMPUTED; WILMS TUMOR;

EID: 0036068165     PISSN: 10774114     EISSN: None     Source Type: Journal    
DOI: 10.1097/00043426-200206000-00013     Document Type: Article

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