Assessment of plasma carnitine concentrations in relation to ceroid lipofuscinosis in Tibetan Terriers

American Journal of Veterinary Research

Volumn 63, Issue 6, 2002, Pages 890-895

  Katz, Martin L ^a   Sanders, Deja A ^a   Sanders, Douglas N ^a   Hansen, Elizabeth A ^a   Johnson, Gary S ^a  

^a UNIVERSITY OF MISSOURI   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

ACYLCARNITINE; CARNITINE; EDETIC ACID; DRUG DERIVATIVE;

AGE; AMINO ACID BLOOD LEVEL; ANIMAL TISSUE; ARTICLE; BLOOD SAMPLING; CASTRATION; CONTROLLED STUDY; DIET RESTRICTION; DOG; FEMALE; GENDER; LIPOFUSCINOSIS; MALE; NONHUMAN; ONSET AGE; SYMPTOMATOLOGY; ANIMAL; ANIMAL DISEASE; BLOOD; BRAIN CORTEX; DOG DISEASE; ELECTRON MICROSCOPY; FLUORESCENCE MICROSCOPY; NEURONAL CEROID LIPOFUSCINOSIS; PATHOLOGY; RETINA; SEX DIFFERENCE; ULTRASTRUCTURE;

ANIMALIA; CANIS FAMILIARIS;

AGE FACTORS; ANIMALS; CARNITINE; CEREBRAL CORTEX; DOG DISEASES; DOGS; FEMALE; MALE; MICROSCOPY, ELECTRON; MICROSCOPY, FLUORESCENCE; NEURONAL CEROID-LIPOFUSCINOSES; RETINA; SEX FACTORS;

EID: 0036017312     PISSN: 00029645     EISSN: None     Source Type: Journal    
DOI: 10.2460/ajvr.2002.63.890     Document Type: Article

References (28)

1. Clinical classification of neuronal ceroid lipofuscinosis subtypes
2. Classification of the neuronal ceroid-lipofuscinoses: Expansion of the atypical forms
3. Neuronal ceroid-lipofuscinoses: The current status
4. Molecular genetics of neuronal ceroid lipofuscinoses
5. Molecular basis of the neurnonal ceroid-lipofuscinoses: Mutations in CLN1, CLN2, CLN3, and CLN5
6. The neuronal ceroid-lipofuscinoses
7. Comparative biology of the neuronal ceroid-lipofuscinoses (NCL): An overview
8. Adult onset lysosomal storage disease in a Tibetan Terrier: Clinical, morphological and biochemical studies
9. The neuronal ceroid-lipofuscinoses: Recent advances
10. The neuronal ceroid-lipofuscinoses (Batten disease): Comparative aspects
11. Lysine methylation of mitochondrial ATP synthase subunit c stored in tissues of dogs with hereditary ceroid-lipofuscinosis
12. Mitochondrial ATP synthase subunit c storage in the ceroid-lipofuscinoses (Batten disease)
13. Mitochondrial ATP synthase subunit c stored in hereditary ceroid-lipofuscinosis contains trimethyllysine
14. Late-infantile ceroidlipofuscinosis: Lysine methylation of mitochondrial subunit c from lysosomal storage bodies
15. Canine hereditary ceroid-lipofuscinosis: Evidence for a defect in the carnitine biosynthetic pathway
16. Decreased plasma carnitine and trimethyl-L-lysine levels associated with lysosomal accumulation of a trimethyl-L-lysine containing protein in Batten disease
17. Tibetan terrier model of canine ceroid lipofuscinosis
18. Assessment of dietary therapies in a canine model of Batten disease
19. Lens luxation and progressive retinal atrophy in the Tibetan terrier
20. Evidence of cell loss from the rat retina during senescence
21. Free and esterified carnitine
22. Myocardial L-carnitine deficiency in a family of dogs with cardiomyopathy
23. Carnitine metabolism during fasting in dogs
24. Carnitine metabolism in human subjects. I. Normal metabolism
25. Age, sex and diabetes-related changes in total, free and acyl carnitine in human plasma
26. L-carnitine administration and withdrawal affect plasma and hepatic carnitine concentrations, plasma lipid and lipoprotein composition, and in vitro hepatic lipogenesis from labeled mevalonate and oleate in normal rabbits
27. Effects of supplementary levels of L-carnitine on blood and urinary carnitines and on the portal-systemic blood-ethanol concentrations in the rat
28. Ascorbic acid and carnitine biosynthesis