Glucose 6-phosphate transport in fibroblast microsomes from glycogen storage disease type 1b patients: Evidence for multiple glucose 6-phosphate transport systems

Biochemical Journal

Volumn 357, Issue 2, 2001, Pages 557-562

  Leuzzi, R ^a   Fulceri, R ^a   Marcolongo, P ^a   Banhegyi G ^a   Zammarchi, E ^a   Stafford, K ^a   Burchell, A ^a   Benedetti, A ^a  

^a UNIVERSITY OF SIENA   (Italy)

Author keywords

Endoplasmic reticulum; Glucose 6 phosphatase system; Glucose 6 phosphate translocase; Hexose phosphate transport system; Von Gierke's disease

Indexed keywords

BIOLOGICAL ORGANS; DISEASES; GENES; GLUCOSE; MUTAGENESIS; PHOSPHATES;

HOMOEOSTASIS;

BIOCHEMISTRY;

CHLOROGENIC ACID; GENE PRODUCT; GLUCOSE 1 PHOSPHATE; GLUCOSE 6 PHOSPHATE; GLUCOSE 6 PHOSPHATE TRANSPORTER; GLYCOGEN; UNCLASSIFIED DRUG;

ARTICLE; CONTROLLED STUDY; ENDOPLASMIC RETICULUM; ENZYME ACTIVITY; FIBROBLAST; GENE MUTATION; GLUCOSE HOMEOSTASIS; GLUCOSE TRANSPORT SYSTEM; GLYCOGEN STORAGE DISEASE TYPE 1; HELA CELL; HUMAN; HUMAN CELL; PHOSPHATE TRANSPORT; PRIORITY JOURNAL;

ANTIPORTERS; BIOLOGICAL TRANSPORT; CELLS, CULTURED; CHLOROGENIC ACID; FIBROBLASTS; GLUCOSE; GLUCOSE-6-PHOSPHATASE; GLUCOSE-6-PHOSPHATE; GLYCOGEN STORAGE DISEASE TYPE I; HUMANS; KINETICS; MICROSOMES; MONOSACCHARIDE TRANSPORT PROTEINS; MUTATION; REFERENCE VALUES; SKIN;

EID: 0035878885     PISSN: 02646021     EISSN: None     Source Type: Journal    
DOI: 10.1042/0264-6021:3570557     Document Type: Article

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