Overexpression of γ-sarcoglycan induces severe muscular dystrophy. Implications for the regulation of sarcoglycan assembly

Journal of Biological Chemistry

Volumn 276, Issue 24, 2001, Pages 21785-21790

  Zhu, Xiaolei ^a   Hadhazy, Michele ^a   Groh, Margaret E ^a   Wheeler, Matthew T ^a   Wollmann, Robert ^a   McNally, Elizabeth M ^a  

^a UNIVERSITY OF CHICAGO   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

BIOLOGICAL MEMBRANES; CARBOHYDRATES; DATA REDUCTION; ENZYME KINETICS; GENETIC ENGINEERING; PROTEINS;

CYTOPLASM; PLASMA MEMBRANES;

BIOCHEMISTRY;

ALPHA SARCOGLYCAN; BETA SARCOGLYCAN; CREATINE KINASE MM; DYSTROPHIN; GAMMA SARCOGLYCAN; SARCOGLYCAN; UNCLASSIFIED DRUG; CYTOSKELETON PROTEIN; DAG1 PROTEIN, HUMAN; DYSTROGLYCAN; MEMBRANE PROTEIN;

ADOLESCENT; ANIMAL MODEL; ANIMAL TISSUE; ARTICLE; CELLULAR DISTRIBUTION; COMPLEX FORMATION; CYTOPLASM; FAST MUSCLE; GENE CONTROL; GENE DISRUPTION; GENE DOSAGE; GENE MUTATION; GENE OVEREXPRESSION; GENE REPLACEMENT THERAPY; LETHALITY; MEMBRANE INSTABILITY; MEMBRANE STABILIZATION; MOUSE; MUSCLE FIBER MEMBRANE; MUSCLE INJURY; MUSCLE MASS; MUSCULAR DYSTROPHY; NONHUMAN; NUCLEOTIDE SEQUENCE; PRIORITY JOURNAL; PROMOTER REGION; PROTEIN ASSEMBLY; PROTEIN FUNCTION; PROTEIN TARGETING; SIGNAL TRANSDUCTION; TRANSGENE; TRANSGENIC MOUSE; ANIMAL; ANIMAL MUSCULAR DYSTROPHY; CATTLE; FAST MUSCLE FIBER; GENE EXPRESSION REGULATION; GENETICS; HEART MUSCLE; METABOLISM; MUTATION; PATHOLOGY; SKELETAL MUSCLE;

ANIMALIA; MURINAE; MUS MUSCULUS;

ANIMALS; CATTLE; CYTOSKELETAL PROTEINS; DYSTROGLYCANS; DYSTROPHIN; GENE EXPRESSION REGULATION; MEMBRANE GLYCOPROTEINS; MICE; MICE, TRANSGENIC; MUSCLE FIBERS, FAST-TWITCH; MUSCLE, SKELETAL; MUSCULAR DYSTROPHY, ANIMAL; MUTATION; MYOCARDIUM; SARCOGLYCANS;

EID: 0035877822     PISSN: 00219258     EISSN: None     Source Type: Journal    
DOI: 10.1074/jbc.M101877200     Document Type: Article

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