A new familial adult-onset leukodystrophy manifesting as cerebellar ataxia and dementia

Journal of the Neurological Sciences

Volumn 183, Issue 1, 2001, Pages 47-55

  Tagawa, Asako ^a   Ono, Seiitsu ^a   Inoue, Kiyoharu ^b   Hosoi, Naoto ^c   Kaneda, Kenshi ^a   Suzuki, Megumi ^a   Nagao, Koichi ^a   Shimizu, Natsue ^a  

^a TEIKYO UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b JIKEI UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^c Sodegaura Satsukidai Hospital   (Japan)

Author keywords

Adult onset; Autosomal dominant; Cerebellar ataxia; Dementia; Leukodystrophy; Vacuolar change

Indexed keywords

ADULT; ARTICLE; AUTOSOMAL DOMINANT INHERITANCE; CASE REPORT; CELL VACUOLE; CEREBELLAR ATAXIA; CLINICAL FEATURE; DEMENTIA; DISEASE COURSE; HISTOPATHOLOGY; HUMAN; LEUKODYSTROPHY; MALE; NUCLEAR MAGNETIC RESONANCE IMAGING; PRIORITY JOURNAL; WHITE MATTER;

ADULT; AGE OF ONSET; ATROPHY; BRAIN; CEREBELLAR ATAXIA; CEREBELLUM; DEMENTIA; FEMALE; FRONTAL LOBE; HUMANS; LEUKODYSTROPHY, GLOBOID CELL; MAGNETIC RESONANCE IMAGING; MALE; MIDDLE AGED; PEDIGREE;

EID: 0035862822     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-510X(00)00472-X     Document Type: Article

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