Confirmation of Mendelian properties of heterodimeric fibrinogen molecules in a heterozygotic dysfibrinogenemia, "fibrinogen Amarillo," using GPRphoresis to differentiate semifibrin molecules from fibrinogen and fibrin

Thrombosis Research

Volumn 101, Issue 2, 2001, Pages 91-99

  Shainoff, John R ^a   Ratnoff, Oscar D ^b   Smejkal, Gary B ^a   DiBello, Patricia M ^a   Welches, William R ^c   Lill, Helmut ^d   Mitkevich, Olga V ^a,e   Periman, Phillip ^f  

^a CLEVELAND STATE UNIVERSITY   (United States)

^b UNIVERSITY HOSPITALS OF CLEVELAND   (United States)

^c South Pointe Hospital   (United States)

^d Roche Diagnostics   (Germany)

^e INSTITUTE OF EXPERIMENTAL CARDIOLOGY   (Russian Federation)

^f Harrington Cancer Center   (United States)

Author keywords

Atroxin; Dysfibrinogenemia; Fibrinogen; GPRphoresis; Semifibrin

Indexed keywords

ARGININE; ATROXIN; DIMER; ENZYME; FIBRIN ANTIBODY; FIBRIN MONOMER; FIBRINOGEN; FIBRINOPEPTIDE A; HISTIDINE; MUTANT PROTEIN; THROMBIN; UNCLASSIFIED DRUG;

ARTICLE; BLOOD CLOTTING DISORDER; CONTROLLED STUDY; DYSFIBRINOGENEMIA; ELECTROPHORESIS; FIBRINOGEN AMARILLO; HETEROZYGOSITY; HUMAN; KINETICS; MUTATION; PHENOTYPE; PRIORITY JOURNAL; PROTEIN LOCALIZATION;

DIMERIZATION; ELECTROPHORESIS, POLYACRYLAMIDE GEL; FAMILY HEALTH; FIBRIN; FIBRINOGENS, ABNORMAL; FIBRINOPEPTIDE A; HETEROZYGOTE; HUMANS; KINETICS; POINT MUTATION; SERINE ENDOPEPTIDASES;

EID: 0035862595     PISSN: 00493848     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0049-3848(00)00383-2     Document Type: Article

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