The presence of a widened vestibular aqueduct and progressive sensorineural hearing loss in the Branchio-Oto-Renal syndrome. A family study

International Journal of Pediatric Otorhinolaryngology

Volumn 59, Issue 3, 2001, Pages 163-172

  Stinckens, Chr ^a   Standaert, L ^b   Casselman, J W ^c   Huygen, P L M ^f   Kumar, S ^d   Van de Wallen, J ^e   Cremers, C W R J ^a,f  

^a UNIVERSITY OF LEUVEN   (Belgium)

^b Royal Institute for the Deaf   (Belgium)

^c University Hospital St Jan   (Belgium)

^d BOYS TOWN NATIONAL RESEARCH HOSPITAL   (United States)

^e GHENT UNIVERSITY HOSPITAL   (Belgium)

^f RADBOUD UNIVERSITY MEDICAL CENTER   (Netherlands)

Author keywords

BOR syndrome; Enlarged vestibular aqueduct; Genetic deafness; Hypoplasia of the cochlea; Progressive sensorineural hearing impairment

Indexed keywords

ARTICLE; BRANCHIOOTORENAL SYNDROME; CHILD; CLINICAL ARTICLE; COMPUTER ASSISTED TOMOGRAPHY; DISEASE COURSE; FAMILY STUDY; FEMALE; HEARING LOSS; HUMAN; MALE; MEDICAL LITERATURE; NUCLEAR MAGNETIC RESONANCE IMAGING; PEDIGREE; PERCEPTION DEAFNESS; PRIORITY JOURNAL; RADIODIAGNOSIS; UNIVERSITY HOSPITAL; VESTIBULE AQUEDUCT;

ADOLESCENT; ADULT; AUDIOMETRY; AUDITORY THRESHOLD; BONE CONDUCTION; BRANCHIO-OTO-RENAL SYNDROME; CHILD; CHILD, PRESCHOOL; DISEASE PROGRESSION; HEARING LOSS, SENSORINEURAL; HUMANS; PEDIGREE; SYNDROME; VESTIBULAR AQUEDUCT;

EID: 0035797094     PISSN: 01655876     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0165-5876(01)00473-6     Document Type: Article

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