Increased anaerobic glycolysis in mitochondrial trifunctional protein-deficient brain

Journal of the Neurological Sciences

Volumn 184, Issue 2, 2001, Pages 197-201

  Miyajima, Hiroaki ^a   Ouchi, Yasuomi ^b   Sakamoto, Masanobu ^b   Takahashi, Yoshitomo ^a   Kono, Satoshi ^a   Suzuki, Hitoshi ^a  

^a HAMAMATSU UNIVERSITY SCHOOL OF MEDICINE   (Japan)

^b HAMAMATSU MEDICAL CENTER   (Japan)

Author keywords

Oxidation; Gene mutation; Glycolysis; Oxidative phosphorylation; Positron emission tomography; Trifunctional protein deficiency

Indexed keywords

ADULT; ALLELE; ANAEROBIC GLYCOLYSIS; ARTICLE; CASE REPORT; FATTY ACID OXIDATION; GENE MUTATION; GLUCOSE METABOLISM; HUMAN; MALE; MITOCHONDRIAL RESPIRATION; MYOGLOBINURIA; OXIDATIVE PHOSPHORYLATION; POLYMERASE CHAIN REACTION; POSITRON EMISSION TOMOGRAPHY; PRIORITY JOURNAL; PROTEIN DEFICIENCY; RHABDOMYOLYSIS;

ADULT; AGED; ALLELES; ANAEROBIOSIS; BRAIN; FEMALE; GLYCOLYSIS; HUMANS; MALE; MIDDLE AGED; MULTIENZYME COMPLEXES; MUTATION; OXYGEN; RHABDOMYOLYSIS; TOMOGRAPHY, EMISSION-COMPUTED;

EID: 0035282837     PISSN: 0022510X     EISSN: None     Source Type: Journal    
DOI: 10.1016/S0022-510X(01)00445-2     Document Type: Article

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