5. Discovery of the hexosaminidase isoenzymes

Advances in Genetics

Volumn 44, Issue , 2001, Pages 43-49

  Robinson, Donald ^a   Stirling, John L ^a  

^a KING'S COLLEGE LONDON   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

BETA N ACETYLHEXOSAMINIDASE;

ANIMAL; ARTICLE; CHEMISTRY; HISTORY; HUMAN; METABOLISM; PROTEIN TERTIARY STRUCTURE; TAY SACHS DISEASE;

ANIMALS; BETA-N-ACETYLHEXOSAMINIDASE; HISTORY, 20TH CENTURY; HUMANS; PROTEIN STRUCTURE, TERTIARY; TAY-SACHS DISEASE;

EID: 0035231161     PISSN: 00652660     EISSN: None     Source Type: Book Series    
DOI: 10.1016/s0065-2660(01)44069-7     Document Type: Review

References (25)

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3. R.O. Brady The sphingolipidoses N. Engl. J. Med. 275 1966 312 318
4. R.O. Brady J.N. Kanfer D. Shapiro Metabolism of glucocerebrosides. II. Evidence of an enzyme deficiency in Gaucher's Disease Biochem. Biophys. Res. Commun. 18 1965 211 225
5. P.J. Carmody M. Ratazzi Conversion of human hexosaminidase A to hexosaminidase B by crude Vibrio cholerae neuraminidase preparations. Merthiolate is the active factor Biochim. Biophys. Acta 371 1974 117 125
6. M. Carroll D. Robinson A low molecular-weight protein cross-reacting with human liver N-acetyl-β- D -hexosaminidase Biochem. J. 137 1974 217 221
7. N. Dance R.G. Price D. Robinson Differential assay of human hexosaminidases A and B Biochim. Biophys. Acta 222 1970 662 664
8. A.J. Furth D. Robinson Specificity and multiple forms of β-galactosidase in the rat Biochem. J. 97 1965 59 66
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22. J.L. Stirling Separation and characterisation of N-acetyl-β-glucosaminidase A and P from maternal serum Biochim. Biophys. Acta 271 1972 154 162
23. L. Svennerholm The chemical structure of normal brain and Tay-Sachs gangliosides Biochem. Biophys. Res. Commun. 9 1962 436 441
24. R.D. Terry S.R. Korey M. Weiss Electron microscopy of the cerebrum in Tay-Sachs disease S.M. Aronson B.W. Volk Cerebral sphingolipidoses 1962 Academic Press New York 49 56
25. E. von Buddecke E. Werries Reinigung und eigenschaften einer-D-acetyl-D-hexosaminidase aus Rindermiltz Z. Naturforsch. 19 1964 798 800