VWF meets the ADAMTS family

Nature Medicine

Volumn 7, Issue 11, 2001, Pages 1177-1178

  Brass, L ^a  

^a UNIVERSITY OF PENNSYLVANIA   (United States)

Author keywords

[No Author keywords available]

Indexed keywords

VON WILLEBRAND FACTOR;

GENE MUTATION; HUMAN; PATHOGENESIS; PATHOPHYSIOLOGY; PRIORITY JOURNAL; SHORT SURVEY; THROMBOCYTE AGGREGATION; THROMBOTIC THROMBOCYTOPENIC PURPURA;

HUMANS; METALLOENDOPEPTIDASES; MODELS, BIOLOGICAL; MUTATION; PURPURA, THROMBOTIC THROMBOCYTOPENIC; VON WILLEBRAND FACTOR;

PURPURA;

EID: 0035173645     PISSN: 10788956     EISSN: None     Source Type: Journal    
DOI: 10.1038/nm1101-1177     Document Type: Short Survey

References (15)

1. Thrombotic thrombocytopenic purpura: Report of 16 cases and a review of the literature
2. Mutations in a member of the ADAMTS gene family cause thrombotic thrombocytopenic purpura
3. Purification of human von Willebrand factor-cleaving protease and its identification as a new member of the metalloproteinase family
4. Partial amino acid sequence of von Willebrand factor-cleaving protease
5. Structure of von Willebrand factor cleaving protease (ADAMTS13), a metalloprotease involved in thrombotic thrombocytopenic purpura
6. Efficacy of intensive plasmapheresis in thrombotic thrombocytopenic purpura
7. Von Willebrand factor
8. Unusually large plasma factor Vlll: Von Willebrand factor multimers in chronic relapsing thrombotic thrombocytopenic purpura
9. Physiologic cleavage of von Willebrand factor by a plasma protease is dependent on its conformation and requires calcium ion
10. Partial purification and characterization of a protease from human plasma cleaving von Willebrand factor to fragments produced by in vivo proteolysis
11. Von Willebrand factor-cleaving protease in thrombotic thrombocytopenic purpura and hemolytic uremic syndrome
12. Antibodies to von Willebrand factor-cleaving protease in acute thrombotic thrombocytopenic purpura
13. Antibody inhibitors to von Willebrand factor metalloproteinase and increased binding of von Willebrand factor to platelets in ticlopidine-associated thrombotic thrombocytopenic purpura
14. Deficient activity of von Willebrand factor-cleaving protease in patients with Upshaw-Schulman syndrome
15. Decrease von Willebrand factor protease activity associated with thrombocytopenic disorders