Very low-density lipoprotein apolipoprotein B-100 turnover in glycogen storage disease type Ia (von Gierke disease)

Journal of Inherited Metabolic Disease

Volumn 24, Issue 5, 2001, Pages 527-534

  Wierzbicki, A S ^a   Watts, G F ^a,b   Lynas, J ^c   Winder, A F ^d   Wray, R ^d  

^a ST THOMAS HOSPITAL   (United Kingdom)

^b UNIVERSITY OF WESTERN AUSTRALIA   (Australia)

^c St Leonards on Sea   (United Kingdom)

^d ROYAL FREE HOSPITAL   (United Kingdom)

Author keywords

[No Author keywords available]

Indexed keywords

APOLIPOPROTEIN B100; FIBRIC ACID DERIVATIVE; GLYCOGEN; INTERMEDIATE DENSITY LIPOPROTEIN; LIPID; LIPOPROTEIN LIPASE; OMEGA 3 FATTY ACID; STARCH; VERY LOW DENSITY LIPOPROTEIN; APOLIPOPROTEIN B; APOLIPOPROTEIN B-100; LACTIC ACID DERIVATIVE; LIPOPROTEIN; LOW DENSITY LIPOPROTEIN;

ADULT; ARTICLE; CLEARANCE; CLINICAL ARTICLE; CLINICAL FEATURE; CONTROLLED STUDY; DIET THERAPY; DISEASE SEVERITY; ENZYME ACTIVATION; ENZYME ACTIVITY; GLYCOGEN STORAGE DISEASE TYPE 1; HUMAN; HUMAN TISSUE; HYPERLIPIDEMIA; INHIBITION KINETICS; LIPOPROTEIN METABOLISM; LIPOPROTEIN SECRETION; LIPOPROTEIN SYNTHESIS; LIVER; LOW FAT DIET; MALE; PANCREATITIS; PREVALENCE; RISK ASSESSMENT; SIBLING; TURNOVER TIME; BLOOD; CARBOHYDRATE DIET; CASE REPORT; DISEASE PREDISPOSITION; GENETICS; GLUCOSE BLOOD LEVEL; METABOLISM;

ADULT; APOLIPOPROTEINS B; BLOOD GLUCOSE; CASE REPORT; DIETARY CARBOHYDRATES; DISEASE SUSCEPTIBILITY; GLYCOGEN STORAGE DISEASE TYPE I; HUMAN; LACTATES; LIPOPROTEINS; LIPOPROTEINS, LDL; LIPOPROTEINS, VLDL; MALE; STARCH;

EID: 0035156751     PISSN: 01418955     EISSN: None     Source Type: Journal    
DOI: 10.1023/A:1012407609063     Document Type: Article

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