Hereditary pure lower motor neuron disease with adult onset and rapid progression

Journal of Neurology

Volumn 248, Issue 4, 2001, Pages 290-296

  Van den Berg Vos, R M ^a   Van den Berg, L H ^a   Jansen, G H ^a   Parton, M ^b   Shaw, C E ^b   Hesseling Janssen, A L W ^c   Wokke, J H J ^a  

^a UNIVERSITY MEDICAL CENTER UTRECHT   (Netherlands)

^b KING'S COLLEGE LONDON   (United Kingdom)

^c ERASMUS MEDICAL CENTER   (Netherlands)

Author keywords

Familial amyotrophic lateral sclerosis; Hereditary; Lower motor neuron disease; Spinal muscular atrophy

Indexed keywords

ADULT; AGED; AMYOTROPHIC LATERAL SCLEROSIS; ARTICLE; AUTOSOMAL DOMINANT DISORDER; CLINICAL ARTICLE; CLINICAL FEATURE; DISEASE COURSE; GLIOSIS; HISTOPATHOLOGY; HUMAN; MALE; MOTOR NEURON DISEASE; MUSCLE WEAKNESS; PRIORITY JOURNAL; RESPIRATORY FAILURE; SPINAL MUSCULAR ATROPHY;

ADULT; AGE OF ONSET; AMYOTROPHIC LATERAL SCLEROSIS; DISEASE PROGRESSION; HUMANS; LEG; MALE; MIDDLE AGED; MOTOR NEURON DISEASE; MUSCLE WEAKNESS; PEDIGREE; PROGNOSIS; RESPIRATORY INSUFFICIENCY; SPINAL CORD; TIME FACTORS;

EID: 0035045978     PISSN: 03405354     EISSN: None     Source Type: Journal    
DOI: 10.1007/s004150170203     Document Type: Article

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